Management of Axillary Contracture in Poland Syndrome: Differentiating Fibrous Band and Skin for Optimal Release

Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-ye...

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Bibliographic Details
Published inJournal of clinical medicine Vol. 12; no. 15; p. 4957
Main Authors Matsuura, Rikako, Shimizu, Yusuke, Matsuura, Naoki, Ntege, Edward Hosea, Wada, Naoki
Format Journal Article
LanguageEnglish
Published Switzerland MDPI AG 28.07.2023
MDPI
Subjects
Asymmetry
Axilla
axillary contracture
Care and treatment
Case Report
Case reports
Case studies
Clinical medicine
Complications and side effects
Contracture
fibrous band
Literature reviews
Poland syndrome
Rehabilitation
Rib cage
Stains & staining
Surgery, Plastic
tendon tissue
Veins & arteries
Z-plasty
Japan
United States > US
tendon tissue
case report
Z-plasty
Poland syndrome
axillary contracture
fibrous band
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Summary:Poland syndrome (PS), an uncommon congenital unilateral aplasia of chest wall muscles, may exhibit rare accompanying signs, such as axillary webbing or contractures. The existing literature on the specific management of axillary contractures is limited. In this report, we present the case of a 10-year-old girl with PS manifesting an axillary web containing a fibrous band, which was successfully surgically corrected by a double-opposing Z-plasty. Our surgical approach entailed a meticulous distinction between the deep fibrous band and the superficial cutaneous layer, guided by histopathological findings that indicated the presence of tendon-like tissue, ultimately yielding excellent outcomes. This report will help expand knowledge by highlighting the unique manifestation of PS and emphasizing the importance of employing appropriate treatment approaches. Moreover, addressing both tendon and skin components is essential for optimal contracture release in PS.
ISSN:2077-0383
2077-0383
DOI:10.3390/jcm12154957