Bicuspid Pulmonary Valve With Atrial Septal Defect Leading to Pulmonary Aneurysm

• Published in: The Annals of thoracic surgery Vol. 93; no. 5; pp. 1706 - 1708
• Main Authors: Goda, Motohiko, MD, Budts, Werner, MD, PhD, Troost, Els, MD, Meyns, Bart, MD, PhD
• Format: Journal Article
• Language: English
• Published: New York, NY Elsevier Inc 01.05.2012; Elsevier
• Subjects: Adult; Anesthesia. Intensive care medicine. Transfusions. Cell therapy and gene therapy; Aneurysm - diagnostic imaging; Aneurysm - etiology; Aneurysm - surgery; Angiography; Biological and medical sciences; Blood and lymphatic vessels; Cardiology. Vascular system; Cardiothoracic Surgery; Congenital heart diseases. Malformations of the aorta, pulmonary vessels and vena cava; Diseases of the peripheral vessels. Diseases of the vena cava. Miscellaneous; Echocardiography, Transesophageal - methods; Female; Follow-Up Studies; Heart; Heart Defects, Congenital - complications; Heart Defects, Congenital - diagnosis; Heart Septal Defects, Atrial - complications; Heart Septal Defects, Atrial - diagnosis; Heart Septal Defects, Atrial - surgery; Humans; Male; Medical sciences; Middle Aged; Mitral Valve - abnormalities; Mitral Valve - surgery; Pneumology; Pulmonary Artery - diagnostic imaging; Pulmonary Valve - abnormalities; Pulmonary Valve - surgery; Pulmonary Valve Stenosis - complications; Pulmonary Valve Stenosis - diagnosis; Pulmonary Valve Stenosis - surgery; Risk Assessment; Surgery; Suture Techniques; Treatment Outcome; Vascular Surgical Procedures - methods; 20; Lung; Aneurysm; Cardiovascular disease; Intracardiac defect; Congenital disease; Pulmonary valve; Vascular disease; Malformation; Heart disease; Atrial septal defect; Anesthesia; Circulatory system; Cardiology
• ISSN: 0003-4975; 1552-6259
• DOI: 10.1016/j.athoracsur.2011.09.063

Pulmonary artery aneurysms are rare. We describe 2 adult patients with pulmonary artery aneurysm with normal pulmonary pressure associated with bicuspid pulmonary valve and atrial septal defect. One patient presented with moderate pulmonary valve stenosis and was treated with open surgery; the other patient had a small atrial septal defect and mild pulmonary valve insufficiency and is periodically still being evaluated. Hemodynamic alterations associated with a pulmonary artery aneurysm are described; the influence of additional volume overload and intrinsic wall abnormalities in pulmonary valvular lesions as potential triggers for the development of these aneurysms are analyzed and therapeutic strategies are discussed.