Bronchoscopic concerns in Proteus syndrome: a case report

Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anes...

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Published inKorean journal of anesthesiology Vol. 69; no. 5; pp. 523 - 526
Main Authors Hong, Jung-Min, Lee, Hyeon Jeong, Kim, Eun Soo, Kim, Hae-Kyu, Jeon, Soeun, Kim, Hyae-Jin
Format Journal Article
LanguageEnglish
Published Korea (South) The Korean Society of Anesthesiologists 01.10.2016
Korean Society of Anesthesiologists
대한마취통증의학회
Subjects
Case Report
difficult intubation
hamartomatous disorder
proteus syndrome
마취과학
Hamartomatous disorder
Proteus syndrome
Difficult intubation
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ISSN2005-6419
2005-7563
DOI10.4097/kjae.2016.69.5.523

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Summary:Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anesthesia in PS patients. An 11-year-old girl with PS was scheduled for ear surgery under general anesthesia. She had features complicating intubation including facial asymmetry and disproportion, abnormal teeth, limitation of neck movement due to torticollis, and thoracolumbar scoliosis. This study reports on a case of deformed airway of a PS patient under fiberoptic bronchoscopy.
Bibliography:ObjectType-Article-1
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G704-000679.2016.69.5.002
ISSN:2005-6419
2005-7563
DOI:10.4097/kjae.2016.69.5.523