Intrathoracic desmoid tumor with invasion of the great vessels

• Published in: European journal of cardio-thoracic surgery Vol. 22; no. 6; pp. 1017 - 1019
• Main Authors: Cardoso, P.F.G., da Silva, L.C.C., Bonamigo, T.P., Geyer, G.
• Format: Journal Article
• Language: English
• Published: Amsterdam Elsevier Science B.V 01.12.2002; Elsevier Science
• Subjects: Adult; Aorta, Thoracic - pathology; Biological and medical sciences; Desmoid; Fibromatosis; Fibromatosis, Aggressive - pathology; Fibromatosis, Aggressive - surgery; Humans; Male; Mediastinal Neoplasms - pathology; Mediastinal Neoplasms - surgery; Mediastinum; Medical sciences; Neoplasm Invasiveness; Pneumology; Surgery; Tumors of the respiratory system and mediastinum; Vena Cava, Superior - pathology; Mediastinum; Surgery; Desmoid; Fibromatosis; Pseudotumor; Human; Mediastinum disease; Blood vessel; Clinical form; Tumor; Benign neoplasm; Desmoid tumor
• ISSN: 1010-7940; 1873-734X
• DOI: 10.1016/S1010-7940(02)00614-0

A desmoid tumor of the mediastinum was diagnosed and treated in a 35-year-old white male who presented with a right supraclavicular mass. He was treated with resection, which involved several vascular structures, requiring multiple vascular reconstructions followed by post-operative radiotherapy. The authors concluded that, when located in the mediastinum, the invasive character of such tumors and its tendency to recur may pose a considerable surgical challenge, requiring careful pre-operative planning and long term post-operative follow -up. The role of radiation therapy is limited to the control of local recurrences.