Extensive congenital abdominal aortic aneurysm and renovascular disease in the neonate

• Published in: Journal of vascular surgery Vol. 55; no. 6; pp. 1762 - 1765
• Main Authors: McAteer, Jarod, MD, Ricca, Robert, MD, Johansen, Kaj H., MD, PhD, Goldin, Adam B., MD, MPH
• Format: Journal Article
• Language: English
• Published: New York, NY Mosby, Inc 01.06.2012; Elsevier
• Subjects: Antihypertensive Agents - therapeutic use; Aortic Aneurysm, Abdominal - congenital; Aortic Aneurysm, Abdominal - diagnosis; Aortic Aneurysm, Abdominal - drug therapy; Aortic Aneurysm, Abdominal - physiopathology; Aortic Aneurysm, Thoracic - congenital; Aortic Aneurysm, Thoracic - diagnosis; Aortic Aneurysm, Thoracic - drug therapy; Aortic Aneurysm, Thoracic - physiopathology; Aortic Rupture - etiology; Aortography - methods; Biological and medical sciences; Blood and lymphatic vessels; Blood Pressure; Cardiology. Vascular system; Diseases of the aorta; Fatal Outcome; Female; Gestational Age; Humans; Hypertension, Renovascular - etiology; Infant, Newborn; Medical sciences; Renal Artery Obstruction - congenital; Renal Artery Obstruction - diagnosis; Renal Artery Obstruction - drug therapy; Renal Artery Obstruction - physiopathology; Renal Circulation; Surgery; Surgery (general aspects). Transplantations, organ and tissue grafts. Graft diseases; Tomography, X-Ray Computed; Ultrasonography, Prenatal; Vascular surgery: aorta, extremities, vena cava. Surgery of the lymphatic vessels; Human; Arterial disease; Vascular disease; Newborn; Congenital; Surgery; Abdominal disease; Cardiovascular disease; Aortic aneurysm; Aortic disease
• ISSN: 0741-5214; 1097-6809
• DOI: 10.1016/j.jvs.2011.12.041

Primary congenital abdominal aortic aneurysm is an extremely rare entity, with only 15 patients reported in the literature. Options for repair are often limited secondary to branch vessel size and other anatomic limitations. We present a neonate diagnosed with an abdominal aortic aneurysm on prenatal ultrasound. A postpartum computed tomography angiogram revealed an extensive type IV thoracoabdominal aortic aneurysm extending to the aortic bifurcation and resulting in bilateral renal artery stenosis. The unique features of this patient and challenges in management are discussed.