Prevalence & features of inner ear malformations among children with congenital sensorineural hearing loss: A Public Cochlear Implant Centre Experience

• Published in: Pakistan journal of medical sciences Vol. 36; no. 7; pp. 1511 - 1516
• Main Authors: Ahmed, Jawwad, Saqulain, Ghulam, Khan, Muhammad Iqbal Javed, Kausar, Mobeen
• Format: Journal Article
• Language: English
• Published: Pakistan Knowledge Bylanes 31.12.2020; AsiaNet Pakistan (Pvt) Ltd; Professional Medical Publications
• Subjects: Age groups; Children; Cochlear implants; Ears & hearing; Gender; Genetic disorders; Hearing loss; Magnetic resonance imaging; Original; Pediatrics; Prognosis; Prostheses and implants; Transplants & implants; Pakistan; Islamabad Pakistan; Middle ear malformations; Computed tomography scan; Prevalence
• ISSN: 1682-024X; 1681-715X
• DOI: 10.12669/pjms.36.7.3134

To determine the prevalence and features of inner ear anomalies in children with congenital profound hearing loss who presented at our cochlear implant center based on imaging studies. This retrospective study reviewed charts of children with congenital SNHL, who presented to Department of Otolaryngology & Auditory Implant Centre, Capital Hospital Islamabad over a period of 2 years from 1 May 2017 to 30 April 2019. These included 481 cases of both genders aged between 1 to 12 years. After gathering demographic data, audiological data, computed tomography findings of the temporal bone were analyzed. Data was analyzed using SPSS 22. The Inner Ear Malformations were identified in 48(10%) children including 28 (58.33%) males and 20 (41.67%) female. Most 20(41.67%) presented at >3-5 years of age followed by 19(39.58%) at 2-3 years. However, no significant association of gender (p=0.57, p=0.076) and age of presentation (p=0.344, p=0.697) for right and left ears was noted with inner ear malformations. The most common anomaly noted were CLA, CH-III and CH-II in decreasing order of frequency in both ears. The prevalence of IEM's was found to be 48(10%). Commonest anomalies noted were CLA, CH-III and CH-II. No significant association of gender and age of presentation was noted with type of anomaly in both ears.