A rare cardiac manifestation in autosomal-dominant polycystic kidney disease
Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder associated with various extrarenal complications. There is little information regarding the occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The major cardiovascular complications of AD...
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Published in | Saudi journal of kidney diseases and transplantation Vol. 28; no. 6; pp. 1443 - 1446 |
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Main Authors | , , , , , , , , , , , , |
Format | Journal Article |
Language | English |
Published |
Riyadh, Saudi Arabia
Saudi Center for Organ Transplantation
01.11.2017
Medknow Publications and Media Pvt. Ltd Medknow Publications & Media Pvt. Ltd Wolters Kluwer Medknow Publications |
Subjects | |
Online Access | Get full text |
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Summary: | Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder
associated with various extrarenal complications. There is little information regarding the
occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The
major cardiovascular complications of ADPKD include valvulopathies and vascular ectasia.
Aneurysm of the atrial septum (ASA) is a very rare manifestation in ADPKD. A 37-year-old
woman who was diagnosed with ADPKD was admitted to our hospital for advanced renal failure.
Pelvic computed tomography revealed multiple variable-sized cysts in both kidneys. Transthoracic
echocardiography showed ASA while the patient was completely asymptomatic |
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ISSN: | 1319-2442 2320-3838 |
DOI: | 10.4103/1319-2442.220844 |