A rare cardiac manifestation in autosomal-dominant polycystic kidney disease

Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder associated with various extrarenal complications. There is little information regarding the occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The major cardiovascular complications of AD...

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Published inSaudi journal of kidney diseases and transplantation Vol. 28; no. 6; pp. 1443 - 1446
Main Authors Jabali, Halah, Mzoughi, Khadijah, Zairi, Ihsan, Bin Fatimah, Layla, Rais, Lamya, Qadduri, Ruqayah, Khidr, Raniya, Kraiem, Sinda, Smaoui, Wided, Krid, Madihah, Beji, Sumayyah, Zouaghi, Karim, Hajji, Maryam
Format Journal Article
LanguageEnglish
Published Riyadh, Saudi Arabia Saudi Center for Organ Transplantation 01.11.2017
Medknow Publications and Media Pvt. Ltd
Medknow Publications & Media Pvt. Ltd
Wolters Kluwer Medknow Publications
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Summary:Autosomal-dominant polycystic kidney disease (ADPKD) is a systemic disorder associated with various extrarenal complications. There is little information regarding the occurrence and distribution of cardiovascular abnormalities during the course of ADPKD. The major cardiovascular complications of ADPKD include valvulopathies and vascular ectasia. Aneurysm of the atrial septum (ASA) is a very rare manifestation in ADPKD. A 37-year-old woman who was diagnosed with ADPKD was admitted to our hospital for advanced renal failure. Pelvic computed tomography revealed multiple variable-sized cysts in both kidneys. Transthoracic echocardiography showed ASA while the patient was completely asymptomatic
ISSN:1319-2442
2320-3838
DOI:10.4103/1319-2442.220844