Abnormal cardiac axis as a prenatal marker of left pulmonary artery sling

Left pulmonary artery sling (LPAS) is a rare vascular anomaly. The left pulmonary artery arises distally from the right pulmonary artery on the right side of the trachea and passes between the trachea and esophagus towards the left lung, compressing the lower trachea. LPAS is associated with congeni...

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Bibliographic Details
Published inPediatrics international Vol. 58; no. 2; pp. 158 - 161
Main Authors Ishii, Yoichiro, Miyamoto, Takashi, Nakajima, Kimiko, Tanaka, Kensuke, Ikeda, Kentaro, Inamura, Noboru, Takagi, Takeshi, Kobayashi, Tomio, Arakawa, Hirokazu
Format Journal Article
LanguageEnglish
Published Australia Blackwell Publishing Ltd 01.02.2016
Subjects
Adult
Airway management
congenital tracheal stenosis
Echocardiography
Electrocardiography
Esophagus
Female
Fetuses
Heart
Heart diseases
Humans
Infant, Newborn
left pulmonary artery sling
Lungs
Male
Middle Aged
Pediatrics
Pregnancy
prenatal screening
Pulmonary arteries
Pulmonary artery
Pulmonary Artery - abnormalities
Pulmonary Artery - diagnostic imaging
Respiratory tract
Stenosis
Trachea
Tracheal Stenosis - etiology
Ultrasonic imaging
Ultrasonography, Prenatal - methods
Ultrasound
Vascular Malformations - complications
Vascular Malformations - diagnosis
left pulmonary artery sling
pulmonary artery
congenital tracheal stenosis
prenatal screening
echocardiography
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Summary:Left pulmonary artery sling (LPAS) is a rare vascular anomaly. The left pulmonary artery arises distally from the right pulmonary artery on the right side of the trachea and passes between the trachea and esophagus towards the left lung, compressing the lower trachea. LPAS is associated with congenital tracheal stenosis, which frequently requires early surgical intervention and has a poor prognosis due to severe airway obstruction after birth. Therefore, LPAS should be prenatally diagnosed to prepare for surgical intervention for tracheal stenosis. To the best of our knowledge, there are few reports on prenatal echocardiographic findings in LPAS. We report three prenatal cases of LPAS, which resulted in respiratory symptoms. We discuss fetal ultrasound findings and highlight the abnormal rotation of the fetal cardiac axis to the right as a useful sign in the prenatal screening of LPAS.
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ISSN:1328-8067
1442-200X
DOI:10.1111/ped.12744