Asymptomatic right atrial leiomyosarcoma with tricuspid valve obstruction in a young female patient

Primary cardiac leiomyosarcomas of the heart are rare tumors usually diagnosed post-mortem. Like other sarcomas located in the heart, it causes symptoms by obstruction or occlusion of cardiac cavities, local invasion, embolization or by systemic manifestations. We present an unusual case of a previo...

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Published inEuropean journal of cardio-thoracic surgery Vol. 14; no. 6; pp. 635 - 638
Main Authors Kornberg, A., Wildhirt, S.M., Kreuzer, E., Reichart, B.
Format Journal Article
LanguageEnglish
Published Amsterdam Elsevier Science B.V 01.12.1998
Elsevier Science
Subjects
Adult
Biological and medical sciences
Cardiology. Vascular system
Combined Modality Therapy
Disease Progression
Female
Heart
Heart Atria
Heart Neoplasms - complications
Heart Neoplasms - therapy
Humans
Leiomyosarcoma - complications
Leiomyosarcoma - therapy
Medical sciences
Tricuspid Valve
Tumors of the heart
Heart tumor
Palliative resection
Cardiac leiomyosarcoma
Adjuvant therapy
Human
Antineoplastic agent
Heart
Palliative surgery
Prognosis
Cardiovascular disease
Asymptomatic
Malignant tumor
Neoadjuvant treatment
Case study
Chemotherapy
Treatment
Heart disease
Young adult
Leiomyosarcoma
Female
Right atrium
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Summary:Primary cardiac leiomyosarcomas of the heart are rare tumors usually diagnosed post-mortem. Like other sarcomas located in the heart, it causes symptoms by obstruction or occlusion of cardiac cavities, local invasion, embolization or by systemic manifestations. We present an unusual case of a previously healthy young female patient who was accidentally diagnosed with a cardiac tumor of unknown origin during routine physical examination in May 1997. Until a few days prior to elective cardiac surgery for diagnostic purposes in June 1997, no clinical symptoms were present. To our surprise, a primary right atrial leiomyosarcoma was found which almost completely occluded the right atrium and destroyed the tricuspid valve. Despite the combination of surgical removal and adjuvant chemotherapy the patient died 3 weeks after the operation due to progressive tumor disease and development of congestive heart failure and lung embolism.
Bibliography:ObjectType-Case Study-2
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ISSN:1010-7940
1873-734X
DOI:10.1016/S1010-7940(98)00243-7