Extensive Melanotic Neuroectodermal Tumor of Infancy

The melanotic neuroectodermal tumor of infancy (MNTI) is a rare childhood neoplasm with an alarming but classical clinical presentation. We present the case of a 2-month-old male infant treated with surgery for an aggressive MNTI on the alveolar process of the maxilla. Radiographic examination showe...

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Published inHead & neck pathology (Totowa, N.J.) Vol. 10; no. 3; pp. 349 - 353
Main Authors Albuquerque, Assis Filipe Medeiros, Cunha, José Ferreira, Avelar, Rafael Linard, Juca, Eduardo, Costa, Fabio Wildson Gurgel, Macedo, Mario Sérgio
Format Journal Article
LanguageEnglish
Published New York Springer US 01.09.2016
Subjects
Biomarkers, Tumor - analysis
Dentistry
Humans
Immunohistochemistry
Infant
Male
Maxillary Neoplasms - pathology
Maxillary Neoplasms - surgery
Medicine
Medicine & Public Health
Neuroectodermal Tumor, Melanotic - pathology
Neuroectodermal Tumor, Melanotic - surgery
Oral and Maxillofacial Surgery
Oral Surgical Procedures
Otorhinolaryngology
Pathology
Sine qua non Clinicopathologic Correlat
Melanotic neuroectodermal tumor of infancy (MNTI)
Surgical excision
Tumor recurrence
Intra-oral mass
Jaw neoplasm
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Summary:The melanotic neuroectodermal tumor of infancy (MNTI) is a rare childhood neoplasm with an alarming but classical clinical presentation. We present the case of a 2-month-old male infant treated with surgery for an aggressive MNTI on the alveolar process of the maxilla. Radiographic examination showed a diffuse osteolytic radiolucent lesion in the right maxilla, and displacement and dysmorphic changes in the developing primary tooth buds. The patient remained well without evidence of recurrence for 6 months after surgery. We discussed clinicopathological features, management alternatives, and outcome.
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ISSN:1936-055X
1936-0568
DOI:10.1007/s12105-015-0671-8