Inflammatory pseudotumor-like follicular dendritic cell sarcoma of the liver

Inflammatory pseudotumor-like follicular dendritic cell sarcoma (IPT-like FDCS) is a rare, low-grade, malignant tumor that mainly involves the spleen and liver, is associated with Epstein-Barr virus and is predominant in middle-aged females. Its histopathology is similar to that seen in inflammatory...

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Published inRevista española de enfermedades digestivas Vol. 113; no. 5; pp. 378 - 379
Main Authors Aparicio Serrano, Ana, Castro Rodríguez, Javier, Gallego Jiménez, Elma, Barrera Baena, Pilar
Format Journal Article
LanguageEnglish
Spanish
Published Spain Sociedad Espanola de Patologia Digestivas 01.05.2021
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Summary:Inflammatory pseudotumor-like follicular dendritic cell sarcoma (IPT-like FDCS) is a rare, low-grade, malignant tumor that mainly involves the spleen and liver, is associated with Epstein-Barr virus and is predominant in middle-aged females. Its histopathology is similar to that seen in inflammatory pseudotumor, but their immunophenotype is different and IPT-like FDCS does not respond to anti-inflammatory drugs. Surgery is the treatment of choice, and chemotherapy or radiation therapy is applied for advanced tumors. A high index of suspicion is needed in presence of large size lesions in the liver or spleen that exhibit a relatively indolent clinical course.
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ISSN:1130-0108
DOI:10.17235/reed.2020.7602/2020