Surgical management of infantile cataracts in dystrophic epidermolysis bullosa

Epidermolysis bullosa describes a group of mechanobullous skin diseases that result in the formation of blisters with little or no trauma. In dystrophic epidermolysis bullosa, the eyelid skin and ocular surface are commonly affected; however, infantile cataracts are a rare occurrence. A 7-month-old...

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Bibliographic Details
Published inJournal of AAPOS Vol. 14; no. 3; pp. 283 - 284
Main Authors Motley, William W., MD, MS, Vanderveen, Deborah K., MD, West, Constance E., MD
Format Journal Article
LanguageEnglish
Published United States Mosby, Inc 01.06.2010
Subjects
Cataract - complications
Cataract Extraction - methods
Epidermolysis Bullosa Dystrophica - complications
Epidermolysis Bullosa Dystrophica - pathology
Eyelids
Humans
Infant
Male
Ophthalmology
Postoperative Complications - pathology
Postoperative Complications - prevention & control
Skin Care - methods
Skin Ulcer - pathology
Skin Ulcer - prevention & control
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Summary:Epidermolysis bullosa describes a group of mechanobullous skin diseases that result in the formation of blisters with little or no trauma. In dystrophic epidermolysis bullosa, the eyelid skin and ocular surface are commonly affected; however, infantile cataracts are a rare occurrence. A 7-month-old boy with dense bilateral cataracts and nystagmus underwent cataract extraction, lens implantation, and limited vitrectomy with the use of specialized techniques to reduce iatrogenic skin and ocular surface complications. No iatrogenic skin or ocular surface complications were observed postoperatively. At 24 months of age, the child demonstrated improved visual function.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
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ISSN:1091-8531
1528-3933
DOI:10.1016/j.jaapos.2010.02.002