Hypoplastic left heart syndrome: from fetus to fontan

The care of children with hypoplastic left heart syndrome is constantly evolving. Prenatal diagnosis of hypoplastic left heart syndrome will aid in counselling of parents, and selected fetuses may be candidates for in utero intervention. Following birth, palliation can be undertaken through staged o...

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Published inCardiology in the young Vol. 28; no. 11; pp. 1275 - 1288
Main Authors Roeleveld, Peter P., Axelrod, David M., Klugman, Darren, Jones, Melissa B., Chanani, Nikhil K., Rossano, Joseph W., Costello, John M.
Format Journal Article
LanguageEnglish
Published Cambridge, UK Cambridge University Press 01.11.2018
Subjects
Child, Preschool
Children
Female
Fetuses
Fontan Procedure - methods
Global Health
Heart
Heart transplantation
Humans
Hypoplastic Left Heart Syndrome - diagnosis
Hypoplastic Left Heart Syndrome - epidemiology
Hypoplastic Left Heart Syndrome - surgery
Immunoglobulins
Infant
Infant, Newborn
Intensive care
International conferences
Morbidity - trends
Mortality
Palliation
Palliative Care
Parents
Patients
Pediatrics
Pregnancy
Prenatal development
Prenatal diagnosis
Prenatal Diagnosis - methods
Review Article
Surgery
Survival Rate - trends
Transplantation
Transplants & implants
critical care management
review
Hypoplastic left heart syndrome
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Summary:The care of children with hypoplastic left heart syndrome is constantly evolving. Prenatal diagnosis of hypoplastic left heart syndrome will aid in counselling of parents, and selected fetuses may be candidates for in utero intervention. Following birth, palliation can be undertaken through staged operations: Norwood (or hybrid) in the 1st week of life, superior cavopulmonary connection at 4–6 months of life, and finally total cavopulmonary connection (Fontan) at 2–4 years of age. Children with hypoplastic left heart syndrome are at risk of circulatory failure their entire life, and selected patients may undergo heart transplantation. In this review article, we summarise recent advances in the critical care management of patients with hypoplastic left heart syndrome as were discussed in a focused session at the 12th International Conference of the Paediatric Cardiac Intensive Care Society held on 9 December, 2016, in Miami Beach, Florida.
Bibliography:ObjectType-Article-2
SourceType-Scholarly Journals-1
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ISSN:1047-9511
1467-1107
DOI:10.1017/S104795111800135X