Osteoglophonic dysplasia: dental and orthodontic implications

• Published in: Orthodontics & craniofacial research Vol. 9; no. 3; pp. 153 - 156
• Main Authors: Roberts, TS, Stephen, L, Beighton, P
• Format: Journal Article
• Language: English
• Published: Oxford, UK Blackwell Publishing Ltd 01.08.2006
• Subjects: Adult; Bone Diseases, Developmental - genetics; case report; craniofacial abnormalities; Craniofacial Abnormalities - genetics; Dentistry; diagnosis; Dwarfism - genetics; Female; growth disorder; Humans; impacted; jaw abnormalities; Mouth Rehabilitation; oral; Orthodontics, Corrective; tooth; Tooth, Impacted - genetics; Tooth, Unerupted - genetics
• ISSN: 1601-6335; 1601-6343
• DOI: 10.1111/j.1601-6343.2006.00369.x

Structured Authors –  Roberts TS, Stephen L, Beighton P Aims and Objectives –  Documentation of dental and orthodontic implications of osteoglophonic dysplasia (OGD). Settings and Participants –  Case report describing oral and dental manifestations of a female with OGD, aged 39 years, who was first documented three decades ago. Results –  This rare genetic disorder manifests with gross stunting of stature, associated with severe craniofacial malformation and multiple unerupted teeth. Radiographically, multiple lucent lesions were present in the tubular bones and mandible as well as several impacted teeth. Conclusion –  We concluded that prosthetic dental replacement in this patient would be difficult because of the distorted jaw relationship and large alveolar ridges. Equally, craniofacial reconstruction might be compromised by obstruction of the nasal airways, difficulty in intubation and postoperative respiratory problems.