Anesthetic experiences of myxoma removal surgery in two patients with Carney complex -A report of two cases
Carney complex is an autosomal dominant disorder that occurs due to a mutation in PRKAR1A, which encodes protein kinase A. The clinical features are multiple endocrine gland neoplasms, skin tumors, pigmented skin lesions, myxomas, and schwannomas. In Carney complex, the cardiac myxoma is a common co...
Saved in:
Published in | Korean journal of anesthesiology Vol. 61; no. 6; pp. 528 - 532 |
---|---|
Main Authors | , |
Format | Journal Article |
Language | English |
Published |
Korea (South)
The Korean Society of Anesthesiologists
01.12.2011
Korean Society of Anesthesiologists 대한마취통증의학회 |
Subjects | |
Online Access | Get full text |
Cover
Loading…
Summary: | Carney complex is an autosomal dominant disorder that occurs due to a mutation in PRKAR1A, which encodes protein kinase A. The clinical features are multiple endocrine gland neoplasms, skin tumors, pigmented skin lesions, myxomas, and schwannomas. In Carney complex, the cardiac myxoma is a common co-morbidity. It occurs in multiples, during young age, regardless of gender and cardiac chamber and is known to recur frequently. Therefore there are high risks of adhesion and massive bleeding due to repeated surgeries. Such surgical risks account for over 50% of disease-specific mortality of Carney complex patients. Here, we present anesthetic experiences of myxoma removal surgery in two patients with Carney complex. |
---|---|
Bibliography: | ObjectType-Article-1 SourceType-Scholarly Journals-1 ObjectType-Feature-2 content type line 23 G704-000679.2011.61.6.006 |
ISSN: | 2005-6419 2005-7563 |
DOI: | 10.4097/kjae.2011.61.6.528 |