Dental root abnormalities in four children with PHACE syndrome

PHACE(S) syndrome is a condition characterized by posterior fossa malformations, hemangiomas, arterial anomalies, cardiac defects, eye abnormalities, sternal cleft, and supraumbilical raphe. We present four children with PHACE(S) syndrome who have absence of or severe malformation of the roots of th...

Full description

Saved in:
Bibliographic Details
Published inPediatric dermatology Vol. 36; no. 4; pp. 505 - 508
Main Authors Youssef, Molly J., Siegel, Dawn H., Chiu, Yvonne E., Drolet, Beth A., Hodgson, Brian D.
Format Journal Article
LanguageEnglish
Published United States Wiley Subscription Services, Inc 01.07.2019
Subjects
Online AccessGet full text

Cover

Loading…
More Information
Summary:PHACE(S) syndrome is a condition characterized by posterior fossa malformations, hemangiomas, arterial anomalies, cardiac defects, eye abnormalities, sternal cleft, and supraumbilical raphe. We present four children with PHACE(S) syndrome who have absence of or severe malformation of the roots of their permanent first molars (PFMs). Root abnormalities in the children's molars were bilateral and not restricted to the segments affected by cutaneous hemangioma. The reason for root abnormalities is unknown, but given the rarity of these findings in healthy children, it is likely an additional dental manifestation of PHACE syndrome. The absence of functional roots in the PFMs can result in significant consequences. Therefore, we recommend a panoramic dental radiograph during transitional dentition for children with PHACE syndrome to screen for dental root abnormalities.
ISSN:0736-8046
1525-1470
DOI:10.1111/pde.13818