Right ventricular noncompaction in a neonate with complex congenital heart disease

• Published in: Cardiology in the young Vol. 15; no. 4; pp. 434 - 436
• Main Authors: Alehan, Dursun, Dogan, Omer Faruk
• Format: Journal Article
• Language: English
• Published: Cambridge, UK Cambridge University Press 01.08.2005
• Subjects: Brief Report; Cardiac arrhythmia; cardiac failure; Cardiology; Cardiomyopathy; Echocardiography; Fatal Outcome; Female; Follow-Up Studies; Heart Defects, Congenital - complications; Heart Defects, Congenital - diagnosis; Heart Defects, Congenital - physiopathology; Heart Failure - diagnosis; Heart Failure - etiology; Heart Failure - physiopathology; Heart Ventricles - abnormalities; Heart Ventricles - diagnostic imaging; Humans; Infant, Newborn; Pulmonary arteries; Radiography, Thoracic; Ventricular Dysfunction, Right - complications; Ventricular Dysfunction, Right - diagnosis; Ventricular Dysfunction, Right - physiopathology; Ventricular Pressure; Cardiomyopathy; echocardiography; cardiac failure
• ISSN: 1047-9511; 1467-1107
• DOI: 10.1017/S1047951105000910

Ventricular noncompaction is a rare unclassified cardiomyopathy occurring because of arrest of the normal intrauterine compaction of the loose luminal component of the ventricular myocardium. There is limited data regarding its diagnosis and outcome in children. It is recognised, however, that right ventricular involvement is extremely rare. We report a case in which only the right ventricular myocardium was noncompacted, a situation which led to heart failure soon after birth.