Large vestibular aqueduct syndrome and stapes fixation

An abnormally large vestibular aqueduct has a well recognized association with inner ear anomalies and it has been assumed previously to be a variant of a Mondini type of deformity (Shuknecht, 1980; Emmett, 1985). The sole radiological finding in some patients with progressive sensorineural loss has...

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Bibliographic Details
Published inJournal of laryngology and otology Vol. 108; no. 11; p. 989
Main Authors Shirazi, A, Fenton, J E, Fagan, P A
Format Journal Article
LanguageEnglish
Published England 01.11.1994
Subjects
Adult
Female
Hearing Loss, Sensorineural - diagnostic imaging
Hearing Loss, Sensorineural - etiology
Hearing Loss, Sensorineural - surgery
Humans
Radiography
Stapes - abnormalities
Stapes Surgery
Syndrome
Vestibular Aqueduct - abnormalities
Vestibular Aqueduct - diagnostic imaging
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Summary:An abnormally large vestibular aqueduct has a well recognized association with inner ear anomalies and it has been assumed previously to be a variant of a Mondini type of deformity (Shuknecht, 1980; Emmett, 1985). The sole radiological finding in some patients with progressive sensorineural loss has been a large vestibular aqueduct (Valvassori and Clemis, 1978; Valvassori, 1983), which is now accepted as a separate clinical entity, i.e. the large vestibular aqueduct syndrome (LVAS). A case is presented which is believed to be the first reported with unilateral LVAS and stapes fixation and also the first stapes gusher described in association with LVAS.
ISSN:0022-2151
DOI:10.1017/S0022215100128695