A rare case of left atrial myxofibromyosarcoma

Myxofibrosarcoma is an aggressive soft tissue sarcoma, previously known as myxoid variant of malignant fibrous histiocytoma. Primary cardiac myxofibrosarcomas are the rarest forms of cardiac malignant tumors that often remain asymptomatic until metastasis occurs. In this case report, we describe a r...

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Bibliographic Details
Published inRadiology case reports Vol. 18; no. 3; pp. 771 - 774
Main Authors Srivastava, Pallavi, Feltrin, Fabricio, Kukkar, Vishal
Format Journal Article
LanguageEnglish
Published Netherlands Elsevier Inc 01.03.2023
Elsevier
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Summary:Myxofibrosarcoma is an aggressive soft tissue sarcoma, previously known as myxoid variant of malignant fibrous histiocytoma. Primary cardiac myxofibrosarcomas are the rarest forms of cardiac malignant tumors that often remain asymptomatic until metastasis occurs. In this case report, we describe a rare left atrial cardiac myxofibrosarcoma in a patient with recurrent renal cell carcinoma. We discuss the multimodality imaging approach to diagnose and evaluate cardiac masses as well as imaging characteristics to differentiate cardiac masses from thrombus.
ISSN:1930-0433
1930-0433
DOI:10.1016/j.radcr.2022.11.047