Management of a child with pulmonary arterial hypertension presenting with systemic hypertension

We describe the course and management of a 12-year-old girl with severe pulmonary arterial hypertension who initially presented with severe systemic hypertension. Successful therapy included pulmonary vasodilators and an atrial septostomy, while ensuring adequate maintenance of her systemic vascular...

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Bibliographic Details
Published inCardiology in the young Vol. 26; no. 2; pp. 378 - 381
Main Authors Flores, Saul, Daily, Joshua, Pratap, Jayant Nick, Cash, Michelle C, Hirsch, Russel
Format Journal Article
LanguageEnglish
Published England Cambridge University Press 01.02.2016
Subjects
Blood Pressure - drug effects
Cardiac Catheterization
Child
Disease Management
Echocardiography
Familial Primary Pulmonary Hypertension - complications
Familial Primary Pulmonary Hypertension - drug therapy
Familial Primary Pulmonary Hypertension - physiopathology
Female
Follow-Up Studies
Humans
Hypertension - complications
Hypertension - drug therapy
Hypertension - physiopathology
Vascular Resistance - physiology
Vasodilator Agents - therapeutic use
paediatrics
systemic hypertension
Pulmonary arterial hypertension
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Summary:We describe the course and management of a 12-year-old girl with severe pulmonary arterial hypertension who initially presented with severe systemic hypertension. Successful therapy included pulmonary vasodilators and an atrial septostomy, while ensuring adequate maintenance of her systemic vascular resistance to maintain cardiac output. Clear understanding of the physiology and judicious medical management in patients with severe pulmonary arterial hypertension using extreme compensatory mechanisms is vitally important.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
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ObjectType-Report-1
ObjectType-Article-3
ISSN:1047-9511
1467-1107
DOI:10.1017/S1047951115001092