Sigmoid volvulus associated with colonic neuronal dysplasia type B in an adolescent

Abstract Sigmoid volvulus is the third leading cause of colon obstruction in adults and is usually associated with chronic intestinal pseudo-obstruction and chronic intractable constipation. In children, it is exceedingly rare, with only sporadic cases reported within patients with Hirschsprung'...

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Published inJournal of pediatric surgery case reports Vol. 1; no. 9; pp. 298 - 300
Main Authors Martínez-Criado, Y, Cabrera-García, R, Moya-Jiménez, M.J, Valladares, J.C, López-Alonso, M
Format Journal Article
LanguageEnglish
Published Elsevier Inc 01.09.2013
Subjects
Constipation
Intestinal neuronal dysplasia
Sigmoid volvulus
Surgery
Constipation
Sigmoid volvulus
Intestinal neuronal dysplasia
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Summary:Abstract Sigmoid volvulus is the third leading cause of colon obstruction in adults and is usually associated with chronic intestinal pseudo-obstruction and chronic intractable constipation. In children, it is exceedingly rare, with only sporadic cases reported within patients with Hirschsprung's disease, prune belly syndrome, pathological aerophagia, chronic constipation and chronic recumbence in neurologically impaired children. Intestinal neuronal dysplasia (IND) type B is a disease of the submucosal plexus of intestine manifesting chronic intestinal obstruction or severe chronic constipation, causing a large bowel dilatation over the years. We report a case of sigmoid volvulus in an adolescent, treated by resection with pathologic findings consistent with NID type B.
ISSN:2213-5766
2213-5766
DOI:10.1016/j.epsc.2013.07.018