Atypical Pityriasis Rubra Pilaris Associated with Arthropathy and Osteoporosis: A Case Report with 15‐Year Follow‐Up

• Published in: Pediatric dermatology Vol. 19; no. 1; pp. 46 - 51
• Main Authors: Behr, Fiona D., Bangert, Jerry L., Hansen, Ronald C.
• Format: Journal Article
• Language: English
• Published: New York, US Blackwell Science, Inc 01.01.2002; Blackwell
• Subjects: Arthritis - complications; Arthritis - diagnostic imaging; Biological and medical sciences; Child; Dermatology; Diagnosis, Differential; Dyskeratosis; Follow-Up Studies; Humans; Keratoderma, Palmoplantar - complications; Male; Medical sciences; Osteolysis - complications; Osteoporosis - complications; Osteoporosis - diagnostic imaging; Pityriasis Rubra Pilaris - complications; Pityriasis Rubra Pilaris - diagnosis; Pityriasis Rubra Pilaris - pathology; Radiography; Skin - pathology; Human; Case study; Hair; Osteoporosis; Skin disease; Association; Diseases of the osteoarticular system; Arthropathy; Pityriasis rubra pilaris; Child
• ISSN: 0736-8046; 1525-1470
• DOI: 10.1046/j.1525-1470.2002.00004.x

Pityriasis rubra pilaris (PRP) is an idiopathic papulosquamous disease that clinically presents with palmoplantar keratoderma and follicular hyperkeratotic papules that coalesce into scaly erythematous plaques. We report a unique case of atypical PRP beginning at 1 year of age with associated severe arthropathy and osteoporosis. We further discuss the clinical and histopathologic aspects of PRP, its possible etiology, and other associated conditions.