Fat Embolism Syndrome in Duchenne Muscular Dystrophy Patients: Early Recognition and Aggressive Therapy

We describe two pediatric patients with Duchenne muscular dystrophy that presented with acute neurologic deterioration and hypoxic respiratory failure requiring mechanical ventilation. These cases fulfill the clinical criteria for Fat Embolism Syndrome. Early recognition and aggressive supportive th...

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Bibliographic Details
Published inCase Reports in Critical Care Vol. 2018; no. 2018; pp. 1 - 4
Main Authors Murphy, Lee D., Lutfi, Riad, Yabrodi, Mouhammad
Format Journal Article
LanguageEnglish
Published Cairo, Egypt Hindawi Publishing Corporation 2018
Hindawi
John Wiley & Sons, Inc
Hindawi Limited
Subjects
Bones
Care and treatment
Case Report
Children
Density
Duchenne muscular dystrophy
Embolism
Health aspects
Medical colleges
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Summary:We describe two pediatric patients with Duchenne muscular dystrophy that presented with acute neurologic deterioration and hypoxic respiratory failure requiring mechanical ventilation. These cases fulfill the clinical criteria for Fat Embolism Syndrome. Early recognition and aggressive supportive therapy with mechanical ventilation, right ventricular afterload reduction, and blood transfusion led to survival without any residual effects from the event. Fat Embolism Syndrome needs to be considered early in the course of patients with Duchenne muscular dystrophy who present with respiratory and neurological symptoms.
Bibliography:Academic Editor: Chiara Lazzeri
ISSN:2090-6420
2090-6439
DOI:10.1155/2018/3686470