Early home management of patients with Pierre Robin Sequence

• Published in: International journal of pediatric otorhinolaryngology Vol. 20; no. 1; pp. 45 - 49
• Main Authors: Olson, Terry S., Kearns, Donald B., Pransky, Seth M., Seid, Allan B.
• Format: Journal Article
• Language: English
• Published: Amsterdam Elsevier Ireland Ltd 01.09.1990; Elsevier
• Subjects: Airway Obstruction - therapy; Biological and medical sciences; Female; Humans; Infant, Newborn; Intubation, Intratracheal - instrumentation; Intubation, Intratracheal - methods; Male; Medical sciences; Nasopharyngeal intubation; Nasopharynx; Otorhinolaryngology. Stomatology; Pierre Robin Syndrome - therapy; Respiratory obstruction; Robin sequence; Time Factors; Robin sequence; Nasopharyngeal intubation; Respiratory obstruction; Case study; Eye disease; Lung function; Malformation; Pierre Robin syndrome; Instrumentation therapy; Obstruction
• ISSN: 0165-5876; 1872-8464
• DOI: 10.1016/0165-5876(90)90333-M

Robin Sequence is a well-described disorder with a reported incidence of 1 in 2000 births. It is characterized by glossoptosis and micrognathia often associated with a cleft palate. Respiratory obstruction at the level of the tongue occurs in many affected children. Prior to routine intensive care unit management, it was the primary factor in the mortality reported in patients with moderately severe to severe deformity. Treatment of this obstruction is controversial and may include a long stay in an intensive care setting. We report two cases that demonstrate properly placed and constructed nasopharyngeal tubes allow a non-surgical treatment with early discharge of the patient and without the risks and morbidity of surgery or the complications of tracheostomy.