Narrative review of assessing the surgical options for double outlet right ventricle

• Published in: Translational pediatrics Vol. 10; no. 1; pp. 165 - 176
• Main Authors: Corno, Antonio F, Durairaj, Saravanan, Skinner, Gregory J
• Format: Journal Article
• Language: English
• Published: China AME Publishing Company 01.01.2021
• Subjects: Review; segmentation; double outlet right ventricle; morphology; congenital heart surgery; Congenital heart defects; three-dimensional reconstruction
• ISSN: 2224-4344; 2224-4336; 2224-4344
• DOI: 10.21037/tp-20-227

The individualized surgical approach in individuals with both arterial trunks arising from the morphologically right ventricle is dictated by the extreme morphological variability encountered in this setting, with each patient being unique. An individualized surgical approach has been designed to take account of the morphological variations, identifying the anatomy with the preoperative three-dimensional CT scan reconstruction. The key features have been considered the distance between tricuspid and pulmonary valves, the size and location of the interventricular communication, and the relationship between the outflow tracts. The surgical approach is tailored, whenever feasible, to create a connection between left ventricle and aorta, but primarily to achieve biventricular repair. Account has been taken of all available surgical options already reported in the literature, identifying the most suitable to provide the best outcomes for each unique morphology. To date, meaningful comparison between different reported surgical series has been difficult because of the marked variation of individual intracardiac morphology, and the lack of reports of specific surgical approaches for well-categorized groups of patients. Our approach, being tailored to the individual cardiac morphology, can be offered to any patient with this ventriculo-arterial connection. Given the difficulties of diagnosis, and the multiple therapeutic indications, very close collaboration between cardiologists and surgeons is indispensable for further progress in the understanding and management of this complex congenital cardiac lesion.