Right iliopsoas kaposiform hemangioendothelioma: a case report

• Published in: The Gazette of the Egyptian Paediatric Association Vol. 72; no. 1; pp. 31 - 5
• Main Authors: Ren, Neng, Gu, Ye, Song, Na, Qian, Wen, Gao, Wenhui, Zhang, Yunfeng
• Format: Journal Article
• Language: English
• Published: Berlin/Heidelberg Springer Berlin Heidelberg 01.12.2024; Springer; Springer Nature B.V; SpringerOpen
• Subjects: Abdomen; Blood platelets; Blood vessels; Bones; Case Report; Case reports; Connective tissue neoplasm; Hemangioma; Hip joint; Iliopsoas muscle; Kaposiform hemangioendothelioma; Kinases; Medicine; Medicine & Public Health; Neonatology; Pediatrics; Skin; Thrombocytopenia; Tumors; Vincristine; Case report; Connective tissue neoplasm; Iliopsoas muscle; Kaposiform hemangioendothelioma
• ISSN: 2090-9942; 1110-6638; 2090-9942
• DOI: 10.1186/s43054-024-00272-4

Background Kaposiform hemangioendothelioma (KHE) is a rare neoplasm of vascular origin. It may involve skin, bone, connective tissue, and parenchymal organs, and it is difficult to make a definite diagnosis in the early stage because Kasabach-Merritt phenomenon may occur in some cases. Case presentation On June 12, 2022, a 19-month boy was admitted to our department with the chief complaint of flexion of the right hip joint for over 1 year. An exploratory laparotomy and pelvic lesion resection were conducted and the resection of the iliopsoas muscle mass was performed. The intraoperative resection of the neoplasm confirmed the pathological diagnosis of kaposiform hemangioendothelioma. The vital signs of the child were stable and recovered well after surgery, and the platelet and coagulation indices were normal. Conclusion KHE is a rare disease in clinics, the number of confirmed cases in the world is still relatively few, and the etiology and mechanism of the disease are still unknown, which could result in misdiagnose and delayed treatment in the disease early stages. It is necessary to continue to collect relevant cases, to unify the standard treatment guidelines as soon as possible, to reduce the mortality rate, and to improve the quality of life of the cases.