Primary pulmonary mucosa-associated lymphoid tissue lymphoma with extensive lung involvement and negative autoimmune and inflammatory background: A case report and literature review

• Published in: Journal of Family & Community Medicine Vol. 31; no. 3; pp. 272 - 274
• Main Authors: Alabdulgader, Abdulrahman I, Nabhan, Arwa A, Althubaity, Arwa M, Alsaid, Abir H, Alsaif, Hind S, Abualola, Hossain A, Al-Mulhim, Mohammed A, Alsayyah, Ahmed A, Aldarweesh, Mohammed I
• Format: Journal Article
• Language: English
• Published: India Medknow Publications and Media Pvt. Ltd 01.07.2024; Wolters Kluwer - Medknow; Wolters Kluwer Medknow Publications
• Subjects: B cells; Bendamustine; Case Report; extranodal marginal zone lymphoma; negative autoimmune mucosa-associated lymphoid tissue lymphoma; primary pulmonary mucosa-associated lymphoid tissue lymphoma; Saudi Arabia; Extranodal marginal zone lymphoma; negative autoimmune mucosa-associated lymphoid tissue lymphoma; primary pulmonary mucosa-associated lymphoid tissue lymphoma
• ISSN: 1319-1683; 2230-8229; 2229-340X
• DOI: 10.4103/jfcm.jfcm_365_23

Primary pulmonary mucosa-associated lymphoid tissue (MALT) lymphoma is a very rare presentation of MALT lymphoma. The presence of a completely negative autoimmune and inflammatory background makes it a real challenge and very rare presentation (probably the second reported case in the literature). We report a case of primary pulmonary MALT lymphoma with negative autoimmune background, demonstrating as multifocal bulky variceal masses causing significant clinical symptoms.