Anomalous Origin of the Left Coronary Artery from the Right Pulmonary Artery

• Published in: Journal of cardiac surgery Vol. 24; no. 1; pp. 49 - 54
• Main Authors: Farouk, Ahmed, Zahka, Kenneth, Siwik, Ernest, Golden, Alex, Karimi, Mohsen, Uddin, Minhaz, Hennein, Hani A.
• Format: Journal Article
• Language: English
• Published: Malden, USA Blackwell Publishing Inc 01.01.2009
• Subjects: Angiography; Coronary Vessel Anomalies - diagnosis; Coronary Vessel Anomalies - surgery; Coronary Vessels - surgery; Echocardiography; Female; Follow-Up Studies; Humans; Infant; Infant, Newborn; Male; Pulmonary Artery - abnormalities; Pulmonary Artery - surgery; Vascular Surgical Procedures - methods
• ISSN: 0886-0440; 1540-8191
• DOI: 10.1111/j.1540-8191.2008.00622.x

Anomalous origin of the left coronary artery (LCA) from the pulmonary artery (ALCAPA) is a rare congenital anomaly, one which requires a high index of suspicion in order to be diagnosed promptly and managed accurately. ALCAPA from the right branch pulmonary artery (RPA) is a small subset of ALCAPA in general, with only a few reported cases in the world literature. We report two cases of ALCAPA from the RPA: the first case, an infant, presented in severe cardiac failure requiring preoperative extracorporeal membrane oxygenation (ECMO) for stabilization; and the second, a neonate, presented with severe aortic coarctation (CoA). Both patients underwent successful complete surgical repair using a modified surgical technique, and are doing well in midterm follow‐up. We describe our operative technique and review the literature of this rare congenital anomaly.