Ventricular Tachycardias and Dilated Cardiomyopathy Caused by Fabry Disease

Women with Fabry disease are considered to have a good prognosis. Here we report the clinical history of a female patient with severe Fabry disease before and after referral to our hospital. She was diagnosed to have a cardiac variant of Fabry disease since a left ventricular endmyocardial biopsy re...

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Bibliographic Details
Published inPacing and clinical electrophysiology Vol. 28; no. 10; pp. 1142 - 1143
Main Authors IGAWA, OSAMU, MIAKE, JUNICHIRO, HISATOME, ICHIRO
Format Journal Article
LanguageEnglish
Published 350 Main Street , Malden , MA 02148‐5018 , USA and 9600 Garsington Road , Oxford OX4 2DQ , UK Blackwell Science Inc 01.10.2005
Subjects
amiodarone
Cardiomyopathy, Dilated - etiology
dilated cardiomyopathy
fabry disease
Fabry Disease - complications
Fatal Outcome
Female
Humans
implantable cardioverter defibrillator
Middle Aged
Tachycardia, Ventricular - etiology
ventricular tachycardia
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Summary:Women with Fabry disease are considered to have a good prognosis. Here we report the clinical history of a female patient with severe Fabry disease before and after referral to our hospital. She was diagnosed to have a cardiac variant of Fabry disease since a left ventricular endmyocardial biopsy revealed specific features of this disease and that cardiac involvement was the sole manifestation. She developed sustained ventricular tachycardia and dilated cardiomyopathy requiring oral administration of amiodarone and a cardiac defibrillator implant.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
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ObjectType-Report-1
ObjectType-Article-3
ISSN:0147-8389
1540-8159
DOI:10.1111/j.1540-8159.2005.00241.x