Acquired Angioedema: A Rare Manifestation of Angioimmunoblastic T Cell Lymphoma

The clinical presentation except age of onset is similar in different types of angioedema. A lymphoproliferative disorder like angioimmunoblastic T cell lymphoma (AITL) rarely presents with symptoms of angioedema. We present extremely rare case of elderly male with recurrent tongue swelling, pruritu...

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Published inIndian journal of otolaryngology, and head, and neck surgery Vol. 71; no. Suppl 1; pp. 96 - 99
Main Authors Bidkar, Vijay G., Rajan, Nita Rachel, Dasar, Santosh, Naik, Ashok S., Rao, Ravikala
Format Journal Article
LanguageEnglish
Published New Delhi Springer India 01.10.2019
Springer Nature B.V
Subjects
Angioedema
Biopsy
Clinical Report
Edema
Head and Neck Surgery
Lymphoma
Medicine
Medicine & Public Health
Otorhinolaryngology
Acquired angioedema
Non Hodgkin lymphoma
Angioimmunoblastic lymphoma
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Summary:The clinical presentation except age of onset is similar in different types of angioedema. A lymphoproliferative disorder like angioimmunoblastic T cell lymphoma (AITL) rarely presents with symptoms of angioedema. We present extremely rare case of elderly male with recurrent tongue swelling, pruritus with normal levels of complements and C1 esterase inhibitor protein featuring as acquired angioedema, a rare manifestation of AITL. Initial response to corticosteroids may be misleading and occurs as a result of immunosuppression of AITL. High index of suspicion may prompt need for histopathological diagnosis of lymph node biopsy. Definitive chemotherapeutic treatment may achieve long term remission.
ISSN:2231-3796
0973-7707
DOI:10.1007/s12070-017-1122-5