A variant of Poland syndrome associated with dextroposition

Poland syndrome is characterized by partial or complete absence of pectoralis muscles, ipsilateral syndactyly, and occasionally other malformations of the anterior chest wall and breast. Other associated anomalies, including dextrocardia, renal malformations, and vertebral anomalies, have been repor...

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Bibliographic Details
Published inJournal of thoracic imaging Vol. 22; no. 4; p. 341
Main Authors Mutlu, Hakan, Sildiroglu, Onur, Basekim, Cinar C, Kizilkaya, Esref
Format Journal Article
LanguageEnglish
Published United States 01.11.2007
Subjects
Adult
Dextrocardia - diagnostic imaging
Diagnosis, Differential
Humans
Male
Poland Syndrome - diagnostic imaging
Tomography, X-Ray Computed
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Summary:Poland syndrome is characterized by partial or complete absence of pectoralis muscles, ipsilateral syndactyly, and occasionally other malformations of the anterior chest wall and breast. Other associated anomalies, including dextrocardia, renal malformations, and vertebral anomalies, have been reported in rare cases. The condition is more frequent among males, and usually occurs on the right hemithorax in the unilateral form. The syndrome is believed to be caused by a genetic disorder that reduces the embryonal circulation in the subclavian and vertebral arteries. We report a 20-year-old man with Poland syndrome on the left hemithorax, which is rarely associated with dextroposition.
ISSN:0883-5993
DOI:10.1097/01.rti.0000184831.84395.05