Anterior cervical corpectomy decompression and fusion for cervical kyphosis in a girl with Ehlers-Danlos syndrome: A case report
Spinal deformities in Ehlers-Danlos syndrome (EDS; type VI) are generally progressive and severe. Surgical treatment has been described for kyphoscoliosis in the thoracolumbar spine. However, there are few studies describing the consequences of an anterior approach in cervical kyphosis. An anterior...
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Published in | World journal of clinical cases Vol. 7; no. 4; pp. 532 - 537 |
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Main Authors | , , , , , , |
Format | Journal Article |
Language | English |
Published |
United States
Baishideng Publishing Group Inc
26.02.2019
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Subjects | |
Online Access | Get full text |
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Summary: | Spinal deformities in Ehlers-Danlos syndrome (EDS; type VI) are generally progressive and severe. Surgical treatment has been described for kyphoscoliosis in the thoracolumbar spine. However, there are few studies describing the consequences of an anterior approach in cervical kyphosis. An anterior approach may not be able to fully decompress the spinal canal and restore the normal curvature of the cervical spine. Therefore, the anterior approach for cervical kyphosis in young children is hard. We describe the first case in an EDS girl with cervical kyphosis who received satisfactory anterior cervical corpectomy decompression and fusion.
The chief complaints of a 16-year-old girl with EDS were double upper limb weakness for 7 years and double lower limb walking instability for 2 years. Moreover, the imaging results revealed that the degree of kyphosis from cervical vertebra 2 to 4 accompanying with spinal cord compression was 30°. An anterior cervical corpectomy involving cervical vertebra 3 and a titanium mesh implant were performed with internal fixation. The results at 3 mo after surgery demonstrated that the anterior fusion was solid, and the kyphosis of the cervical spine was corrected. Additionally, the power of all four extremities was significantly improved.
The incidence rate of cervical kyphosis in EDS is rare. The surgical treatment for these patients, especially an anterior approach, is challenging. Therefore, to develop safer and more effective strategies to treat cervical kyphosis in EDS, there is still much work to do. |
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Bibliography: | Corresponding author: Rui He, MD, Chief Doctor, Department of Spinal Surgery, The First Affiliated Hospital of USTC, No. 1, Swan Lake Road, Zhengwu District, Hefei 230000, Anhui Province, China. herui2005208@sina.com Telephone: 13966731701 Author contributions: He R, Fang H, Liu PF, Ge C, Zhang WZ, Shang XF, and Shen CL examined the patient and collected the clinical data; He R performed the surgery and analyzed the radiologic imaging data; Fang H wrote the paper. |
ISSN: | 2307-8960 2307-8960 |
DOI: | 10.12998/wjcc.v7.i4.532 |