Neurocutaneous melanosis associated with Dandy-Walker malformation

Neurocutaneous melanosis is an uncommon congenital disorder consisting of benign or malignant melanocytic tumors of the leptomeninges with large or numerous cutaneous congenital melanocytic nevi. The Dandy-Walker malformation occurs as an enlarged posterior fossa with high insertion of the tentorium...

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Bibliographic Details
Published inActa neurochirurgica Vol. 148; no. 10; pp. 1103 - 1106
Main Authors Kalayci, M, Cağavi, F, Bayar, U, Gül, S, Dursun, A, Ermis, B, Açikgöz, B
Format Journal Article
LanguageEnglish
Published Austria Springer Nature B.V 01.10.2006
Subjects
Congenital diseases
Dandy-Walker Syndrome - complications
Dandy-Walker Syndrome - diagnosis
Female
Humans
Infant, Newborn
Melanosis - complications
Melanosis - diagnosis
Neurocutaneous Syndromes - complications
Neurocutaneous Syndromes - diagnosis
Tentorium
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Summary:Neurocutaneous melanosis is an uncommon congenital disorder consisting of benign or malignant melanocytic tumors of the leptomeninges with large or numerous cutaneous congenital melanocytic nevi. The Dandy-Walker malformation occurs as an enlarged posterior fossa with high insertion of the tentorium, hypoplasia or aplasia of the cerebellar vermis, and cystic dilatation of the fourth ventricle. To our knowledge, the association of these two conditions has been reported only 14 times. In this article, we present a newborn patient with neurocutaneous melanosis associated with Dandy-Walker malformation, which was diagnosed by magnetic resonance imaging.
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ISSN:0001-6268
0942-0940
DOI:10.1007/s00701-006-0739-z