A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management

Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutrition...

Full description

Saved in:
Bibliographic Details
Published inClinical nutrition (Edinburgh, Scotland) Vol. 39; no. 2; pp. 343 - 352
Main Authors Salera, Simona, Tadini, Gianluca, Rossetti, Donata, Grassi, Francesca Sofia, Marchisio, Paola, Agostoni, Carlo, Giavoli, Claudia, Rodari, Giulia, Guez, Sophie
Format Journal Article
LanguageEnglish
Published England Elsevier Ltd 01.02.2020
Subjects
Enteral nutrition
Epidermolysis bullosa
Growth retardation
Hypercatabolism
Nutritional status
Undernutrition
Epidermolysis bullosa
Enteral nutrition
Hypercatabolism
Undernutrition
Growth retardation
Nutritional status
Online AccessGet full text

Cover

Abstract Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.
AbstractList Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.
Author Giavoli, Claudia
Salera, Simona
Marchisio, Paola
Agostoni, Carlo
Rodari, Giulia
Guez, Sophie
Grassi, Francesca Sofia
Rossetti, Donata
Tadini, Gianluca
Author_xml – sequence: 1
  givenname: Simona
  surname: Salera
  fullname: Salera, Simona
  email: simona.salera@policlinico.mi.it
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
– sequence: 2
  givenname: Gianluca
  surname: Tadini
  fullname: Tadini, Gianluca
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
– sequence: 3
  givenname: Donata
  surname: Rossetti
  fullname: Rossetti, Donata
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
– sequence: 4
  givenname: Francesca Sofia
  surname: Grassi
  fullname: Grassi, Francesca Sofia
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
– sequence: 5
  givenname: Paola
  surname: Marchisio
  fullname: Marchisio, Paola
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
– sequence: 6
  givenname: Carlo
  orcidid: 0000-0002-5006-0832
  surname: Agostoni
  fullname: Agostoni, Carlo
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Media Intensità di Cura, 20122, Milano, Italy
– sequence: 7
  givenname: Claudia
  surname: Giavoli
  fullname: Giavoli, Claudia
  organization: Dipartimento di Scienze Cliniche e di Comunità, Università degli Studi di Milano, 20122, Milano, Italy
– sequence: 8
  givenname: Giulia
  surname: Rodari
  fullname: Rodari, Giulia
  organization: Dipartimento di Scienze Cliniche e di Comunità, Università degli Studi di Milano, 20122, Milano, Italy
– sequence: 9
  givenname: Sophie
  surname: Guez
  fullname: Guez, Sophie
  organization: Fondazione IRCCS Ca’ Granda Ospedale Maggiore Policlinico, Pediatria Alta Intensità di Cura, 20122, Milano, Italy
BackLink https://www.ncbi.nlm.nih.gov/pubmed/30857908$$D View this record in MEDLINE/PubMed
BookMark eNp9kEtrHDEQhEWwsdeO_0AOQcccMuuWNC-FXMySFxhySc5C0vQkWmaktXrG4H8frdfJMVDQFFQX1HfFzmKKyNgbAVsBor3db_0U160Eobcgi9QrthGNkpXQvTpjG5CtqJpW1JfsimgPAI3q-gt2qaBvOg39huEdj-uSwxJSrJwlHLg9HHKy_jdfEsdDGDDPaXqiQNyt05TIfuA7uxLSe26pHJoxLsVkfFhDxmfHbRz4bKP99exfs_PRToQ3L_ea_fz86cfua3X__cu33d195VXTLlVbN51zYw8KFHohG68G6d2AXT06NVpX-w76XsvGdbXwoxZCeWsd6rbVWnfqmr079ZYFDyvSYuZAHqfJRkwrGSk01H0N9TEqT1GfE1HG0RxymG1-MgLMEa_ZmyNec8RrQBap8vT2pX91Mw7_Xv7yLIGPpwCWlY8BsyEfMHocChm_mCGF__X_AQrDj0Y
CitedBy_id crossref_primary_10_1080_14728214_2020_1839049
crossref_primary_10_3389_fsurg_2023_1189962
crossref_primary_10_1186_s13023_023_02870_8
crossref_primary_10_20960_nh_04827
crossref_primary_10_1016_j_jhsa_2023_10_022
crossref_primary_10_1111_2047_3095_12364
crossref_primary_10_15690_vsp_v20i5_2315
crossref_primary_10_20960_nh_04330
crossref_primary_10_36106_gjra_6008367
crossref_primary_10_1111_bjd_18624
crossref_primary_10_1016_S1761_2896_24_49118_8
crossref_primary_10_1080_09546634_2024_2350232
crossref_primary_10_1111_1346_8138_16955
crossref_primary_10_3389_fmed_2020_576558
crossref_primary_10_1371_journal_pone_0274072
Cites_doi 10.3390/nu9060594
10.1016/j.det.2010.01.007
10.1111/j.1525-1470.2011.01612.x
10.1111/ijd.12876
10.1186/1750-1172-9-76
10.1016/j.jaad.2009.03.053
10.1111/j.1365-2133.2005.07123.x
10.1016/j.jaad.2009.03.052
10.1186/s12887-016-0714-7
10.3390/nu9091032
10.1111/j.1525-1470.1988.tb00879.x
10.1111/j.1365-2133.1996.tb03840.x
10.1111/j.1525-1470.2010.01127.x
10.1111/bjd.16139
10.1002/ajmg.a.31873
10.3945/an.112.003608
10.1111/1523-1747.ep12471769
10.1590/abd1806-4841.20153206
10.1111/j.1468-3083.2004.01067.x
10.1097/MOP.0000000000000380
10.1111/j.1365-2230.2011.04091.x
10.1016/j.jpedsurg.2011.02.017
10.1007/s40272-014-0086-0
10.1016/S0002-8223(95)00157-3
10.1055/s-0034-1391308
10.1111/j.1365-2133.1996.tb06318.x
10.1067/mpd.2002.123287
10.1097/MPG.0b013e31812f5667
10.2214/AJR.11.8159
10.1016/j.jaad.2010.08.028
10.1097/MPG.0000000000000256
10.1111/pde.12262
10.1002/ajmg.a.36654
10.1016/j.jpeds.2013.08.004
10.1001/archderm.1989.01670150064009
10.1016/j.det.2010.01.006
10.3349/ymj.2014.55.1.264
10.1016/j.det.2010.01.010
10.1046/j.1525-1470.2003.20404.x
10.1111/j.1365-2133.2011.10592.x
10.1097/PHM.0000000000000205
10.1111/j.1365-2133.2008.08507.x
10.1007/s00383-007-2100-x
ContentType Journal Article
Copyright 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism
Copyright © 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism. All rights reserved.
Copyright_xml – notice: 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism
– notice: Copyright © 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism. All rights reserved.
DBID NPM
AAYXX
CITATION
7X8
DOI 10.1016/j.clnu.2019.02.023
DatabaseName PubMed
CrossRef
MEDLINE - Academic
DatabaseTitle PubMed
CrossRef
MEDLINE - Academic
DatabaseTitleList PubMed
Database_xml – sequence: 1
  dbid: NPM
  name: PubMed
  url: https://proxy.k.utb.cz/login?url=http://www.ncbi.nlm.nih.gov/entrez/query.fcgi?db=PubMed
  sourceTypes: Index Database
DeliveryMethod fulltext_linktorsrc
Discipline Medicine
Diet & Clinical Nutrition
EISSN 1532-1983
EndPage 352
ExternalDocumentID 10_1016_j_clnu_2019_02_023
30857908
S0261561419300779
Genre Journal Article
Review
GroupedDBID ---
--K
--M
.1-
.FO
.GJ
.~1
0R~
1B1
1P~
1RT
1~.
1~5
29B
4.4
457
4G.
53G
5GY
5VS
6PF
7-5
71M
8P~
9JM
AABNK
AACTN
AAEDT
AAEDW
AAIAV
AAIKJ
AAKOC
AALRI
AAOAW
AAQFI
AAQXK
AAWTL
AAXUO
ABBQC
ABJNI
ABLJU
ABLVK
ABMAC
ABMZM
ABXDB
ABYKQ
ACDAQ
ACGFS
ACJTP
ACRLP
ADBBV
ADEZE
ADHUB
ADMUD
AEBSH
AEKER
AENEX
AEVXI
AFCTW
AFKWA
AFRHN
AFTJW
AFXBA
AFXIZ
AGHFR
AGUBO
AGYEJ
AHHHB
AIEXJ
AIKHN
AISVY
AITUG
AJBFU
AJOXV
AJRQY
AJUYK
ALMA_UNASSIGNED_HOLDINGS
AMFUW
AMRAJ
ANZVX
ASPBG
AVWKF
AXJTR
AZFZN
BKOJK
BLXMC
BNPGV
CAG
COF
CS3
DU5
E.L
EBS
EFJIC
EFLBG
EJD
EO8
EO9
EP2
EP3
F5P
FDB
FEDTE
FGOYB
FIRID
FNPLU
FYGXN
G-2
G-Q
GBLVA
HDZ
HMK
HMO
HVGLF
HZ~
IHE
J1W
KOM
LCYCR
LZ1
M29
M2W
M41
MO0
N9A
NAHTW
O-L
O9-
OAUVE
OC.
ON0
OZT
P-8
P-9
P2P
PC.
Q38
R2-
RIG
ROL
RPZ
SAE
SCC
SDF
SDG
SEL
SES
SEW
SNG
SNH
SPCBC
SSH
SSZ
T5K
UAP
UHS
UV1
WUQ
Z5R
ZGI
~G-
AAHBH
AAXKI
ADVLN
AFJKZ
AKRWK
NPM
AAYXX
CITATION
7X8
ID FETCH-LOGICAL-c356t-6457bbf80303ec125c3d2cbde74fb3fab4c7088925b741cf9113caabe96699973
IEDL.DBID .~1
ISSN 0261-5614
IngestDate Thu Oct 24 22:03:15 EDT 2024
Thu Sep 26 15:36:42 EDT 2024
Sat Sep 28 08:30:57 EDT 2024
Fri Feb 23 02:48:36 EST 2024
IsPeerReviewed true
IsScholarly true
Issue 2
Keywords Epidermolysis bullosa
Enteral nutrition
Hypercatabolism
Undernutrition
Growth retardation
Nutritional status
Language English
License Copyright © 2019 Elsevier Ltd and European Society for Clinical Nutrition and Metabolism. All rights reserved.
LinkModel DirectLink
MergedId FETCHMERGED-LOGICAL-c356t-6457bbf80303ec125c3d2cbde74fb3fab4c7088925b741cf9113caabe96699973
Notes ObjectType-Article-2
SourceType-Scholarly Journals-1
ObjectType-Feature-3
content type line 23
ObjectType-Review-1
ORCID 0000-0002-5006-0832
PMID 30857908
PQID 2190484047
PQPubID 23479
PageCount 10
ParticipantIDs proquest_miscellaneous_2190484047
crossref_primary_10_1016_j_clnu_2019_02_023
pubmed_primary_30857908
elsevier_sciencedirect_doi_10_1016_j_clnu_2019_02_023
PublicationCentury 2000
PublicationDate February 2020
2020-Feb
2020-02-00
20200201
PublicationDateYYYYMMDD 2020-02-01
PublicationDate_xml – month: 02
  year: 2020
  text: February 2020
PublicationDecade 2020
PublicationPlace England
PublicationPlace_xml – name: England
PublicationTitle Clinical nutrition (Edinburgh, Scotland)
PublicationTitleAlternate Clin Nutr
PublicationYear 2020
Publisher Elsevier Ltd
Publisher_xml – name: Elsevier Ltd
References Haapala, Peterson, Daunter, Hurvitz (bib40) 2015 Jul; 94
Martinez, Mellerio (bib26) 2010 Apr; 28
Ingen-Housz-Oro, Blanchet-Bardon, Vrillat, Dubertret (bib31) 2004 Nov; 18
Freeman, Köglmeier, Martinez, Mellerio, Haynes, Sebire (bib8) 2008 Jun; 158
El Hachem, Zambruno, Bourdon-Lanoy, Ciasulli, Buisson, Hadj-Rabia (bib1) 2014 May 20; 9
Rodari, Guez, Manzoni, Chalouhi, Profka, Bergamaschi (bib28) 2016 Dec 23
Heyman, Zwass, Applebaum, Gordon, Ring (bib14) 1993 Jun; 88
Eismann, Lucky, Cornwall (bib18) 2014 Mar 1; 31
European Food Safety Authority (EFSA) (bib39) 2010; 8
Haynes (bib44) 2008
De Cosmi, Milani, Mazzocchi, D'Oria, Silano, Calderini (bib32) 2017 Sep 18; 9
Hoover-Fong, McGready, Schulze, Barnes, Scott (bib53) 2007 Oct 1; 143A
Quick, Byrd-Bredbenner, Neumark-Sztainer (bib19) 2013 May 1; 4
ISCD (bib42) 2013
Stehr, Farrell, Lucky, Johnson, Racadio, Azizkhan (bib49) 2008 Mar 20; 24
Murat-Sušić, Husar, Skerlev, Marinović, Babić (bib3) 2011; vol. 19
Haynes (bib16) 2010 Apr; 28
De Angelis, Caldaro, Torroni, Romeo, Foschia, di Abriola (bib11) 2011 May; 46
Zanini, Guez, Salera, Farris, Morandi, Gentilino (bib12) 2014 Oct 20; 16
West, Yang, Weitzenkamp, Andrews, Meaney, Oleszek (bib52) 2013 Dec 1; 163
Hubbard (bib45) 2016 Feb; 55
Salera, Menni, Moggio, Guez, Sciacco, Esposito (bib41) 2017 Jun 10; 9
Zidorio, Dutra, Leão, Costa (bib7) 2015 Apr; 90
Vowinkel, Laukoetter, Mennigen, Hahnenkamp, Gottschalk, Boschin (bib50) 2015 Jan 15; 47
Haynes (bib2) 2007
Fine, Tamura, Johnson (bib35) 1989 Mar; 125
Lechner-Gruskay, Honig, Pereira, McKinney (bib25) 1988 Feb; 5
De Giuseppe, Venturelli, Guez, Salera, De Vita, Consonni (bib36) 2016 Dec 29; 16
Reyes, Cattani, Gajardo, García, McGrath, Palisson (bib29) 2002 Apr; 140
Melville, Atherton, Burch, Cohn, Sullivan (bib37) 1996 Oct; 135
Fine, Mellerio (bib5) 2009 Sep; 61
Haynes, Atherton, Ade-Ajayi, Wheeler, Kiely (bib46) 1996 May; 134
Cohn, Teng (bib43) 2016 Aug; 28
Lara-Corrales, Mellerio, Martinez, Green, Lucky, Azizkhan (bib38) 2010 May; 27
Zidorio, Dutra, Castro, Carvalho (bib51) 2018 Apr 17
Colomb, Bourdon-Lannoy, Lambe, Sauvat, Hadj Rabia, Teillac (bib24) 2012 Feb; 166
Martinez, Allgrove, Brain (bib23) 2010 Apr; 28
Fewtrell, Allgrove, Gordon, Brain, Atherton, Harper (bib30) 2006 May; 154
Cunnane, Kent, McAdoo, Caldwell, Lin, Carter (bib34) 1987 Oct; 89
Department of Health and Social Security (bib33) 1971; 127
Beets, Rodríguez-Fonseca, Hennekam (bib54) 2014 Sep 1; 164
Kim, Namgung, Lee, Kim, Eun, Park (bib22) 2014 Jan; 55
Haynes, Mellerio, Martinez (bib47) 2012 May; 29
Sklar, Haynes (bib15) 2014
Birge (bib21) 1995 May; 95
Fine, Mellerio (bib4) 2009 Sep; 61
Fine, Johnson, Weiner, Suchindran (bib10) 2008 Feb; 46
Bruckner, Bedocs, Keiser, Tang, Doernbrack, Arbuckle (bib27) 2011 Nov; 65
Patel, Wells, Jones, Browne, Moss, Parikh (bib48) 2014 May; 58
Haynes (bib6) 2007
Annicchiarico, Morgese, Brunetti, Tampoia, Garofalo, Aceto (bib17) 2012 Oct; 16
Hubbard, Haynes, Sklar, Martinez, Mellerio (bib9) 2011 Aug; 36
Fox, Alderdice, Atherton (bib20) 2003; 20
Spiliopoulos, Sabharwal, Krokidis, Gkoutzios, Mellerio, Dourado (bib13) 2012 Jul; 199
Murat-Sušić (10.1016/j.clnu.2019.02.023_bib3) 2011; vol. 19
Haapala (10.1016/j.clnu.2019.02.023_bib40) 2015; 94
Zidorio (10.1016/j.clnu.2019.02.023_bib7) 2015; 90
Cunnane (10.1016/j.clnu.2019.02.023_bib34) 1987; 89
West (10.1016/j.clnu.2019.02.023_bib52) 2013; 163
Ingen-Housz-Oro (10.1016/j.clnu.2019.02.023_bib31) 2004; 18
Haynes (10.1016/j.clnu.2019.02.023_bib16) 2010; 28
Fine (10.1016/j.clnu.2019.02.023_bib4) 2009; 61
Eismann (10.1016/j.clnu.2019.02.023_bib18) 2014; 31
Martinez (10.1016/j.clnu.2019.02.023_bib26) 2010; 28
Colomb (10.1016/j.clnu.2019.02.023_bib24) 2012; 166
Fine (10.1016/j.clnu.2019.02.023_bib35) 1989; 125
Reyes (10.1016/j.clnu.2019.02.023_bib29) 2002; 140
De Cosmi (10.1016/j.clnu.2019.02.023_bib32) 2017; 9
Bruckner (10.1016/j.clnu.2019.02.023_bib27) 2011; 65
Rodari (10.1016/j.clnu.2019.02.023_bib28) 2016
Lara-Corrales (10.1016/j.clnu.2019.02.023_bib38) 2010; 27
Kim (10.1016/j.clnu.2019.02.023_bib22) 2014; 55
Martinez (10.1016/j.clnu.2019.02.023_bib23) 2010; 28
Quick (10.1016/j.clnu.2019.02.023_bib19) 2013; 4
Hubbard (10.1016/j.clnu.2019.02.023_bib45) 2016; 55
Haynes (10.1016/j.clnu.2019.02.023_bib2) 2007
Lechner-Gruskay (10.1016/j.clnu.2019.02.023_bib25) 1988; 5
Beets (10.1016/j.clnu.2019.02.023_bib54) 2014; 164
Cohn (10.1016/j.clnu.2019.02.023_bib43) 2016; 28
Hubbard (10.1016/j.clnu.2019.02.023_bib9) 2011; 36
Vowinkel (10.1016/j.clnu.2019.02.023_bib50) 2015; 47
Zidorio (10.1016/j.clnu.2019.02.023_bib51) 2018
ISCD (10.1016/j.clnu.2019.02.023_bib42) 2013
Heyman (10.1016/j.clnu.2019.02.023_bib14) 1993; 88
European Food Safety Authority (EFSA) (10.1016/j.clnu.2019.02.023_bib39) 2010; 8
Haynes (10.1016/j.clnu.2019.02.023_bib47) 2012; 29
Haynes (10.1016/j.clnu.2019.02.023_bib44) 2008
Spiliopoulos (10.1016/j.clnu.2019.02.023_bib13) 2012; 199
Fewtrell (10.1016/j.clnu.2019.02.023_bib30) 2006; 154
Zanini (10.1016/j.clnu.2019.02.023_bib12) 2014; 16
Salera (10.1016/j.clnu.2019.02.023_bib41) 2017; 9
Sklar (10.1016/j.clnu.2019.02.023_bib15) 2014
Freeman (10.1016/j.clnu.2019.02.023_bib8) 2008; 158
Birge (10.1016/j.clnu.2019.02.023_bib21) 1995; 95
Fox (10.1016/j.clnu.2019.02.023_bib20) 2003; 20
Department of Health and Social Security (10.1016/j.clnu.2019.02.023_bib33) 1971; 127
Annicchiarico (10.1016/j.clnu.2019.02.023_bib17) 2012; 16
Haynes (10.1016/j.clnu.2019.02.023_bib6) 2007
Stehr (10.1016/j.clnu.2019.02.023_bib49) 2008; 24
Hoover-Fong (10.1016/j.clnu.2019.02.023_bib53) 2007; 143A
El Hachem (10.1016/j.clnu.2019.02.023_bib1) 2014; 9
De Angelis (10.1016/j.clnu.2019.02.023_bib11) 2011; 46
Patel (10.1016/j.clnu.2019.02.023_bib48) 2014; 58
Fine (10.1016/j.clnu.2019.02.023_bib5) 2009; 61
Haynes (10.1016/j.clnu.2019.02.023_bib46) 1996; 134
Fine (10.1016/j.clnu.2019.02.023_bib10) 2008; 46
Melville (10.1016/j.clnu.2019.02.023_bib37) 1996; 135
De Giuseppe (10.1016/j.clnu.2019.02.023_bib36) 2016; 16
References_xml – volume: 20
  start-page: 303
  year: 2003
  end-page: 306
  ident: bib20
  article-title: Are children with recessive dystrophic epidermolysis bullosa of low birthweight?
  publication-title: Pediatr Dermatol
  contributor:
    fullname: Atherton
– volume: 55
  start-page: 181
  year: 2016 Feb
  end-page: 186
  ident: bib45
  article-title: Long-term outcomes in adults with recessive dystrophic epidermolysis bullosa fed by a gastrostomy tube in situ
  publication-title: Int J Dermatol
  contributor:
    fullname: Hubbard
– volume: 47
  start-page: 541
  year: 2015 Jan 15
  end-page: 544
  ident: bib50
  article-title: A two-step multidisciplinary approach to treat recurrent esophageal strictures in children with epidermolysis bullosa dystrophica
  publication-title: Endoscopy
  contributor:
    fullname: Boschin
– volume: 9
  start-page: 594
  year: 2017 Jun 10
  ident: bib41
  article-title: Nutritional challenges in duchenne muscular dystrophy
  publication-title: Nutrients
  contributor:
    fullname: Esposito
– volume: 95
  start-page: 575
  year: 1995 May
  end-page: 579
  ident: bib21
  article-title: Nutrition management of patients with epidermolysis bullosa
  publication-title: J Am Diet Assoc
  contributor:
    fullname: Birge
– volume: 134
  start-page: 872
  year: 1996 May
  end-page: 879
  ident: bib46
  article-title: Gastrostomy and growth in dystrophic epidermolysis bullosa
  publication-title: Br J Dermatol
  contributor:
    fullname: Kiely
– volume: 61
  start-page: 387
  year: 2009 Sep
  end-page: 402
  ident: bib5
  article-title: Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part II. Other organs
  publication-title: J Am Acad Dermatol
  contributor:
    fullname: Mellerio
– start-page: 690
  year: 2014
  end-page: 705
  ident: bib15
  publication-title: Clinical paediatric dietetics
  contributor:
    fullname: Haynes
– volume: 154
  start-page: 959
  year: 2006 May
  end-page: 962
  ident: bib30
  article-title: Bone mineralization in children with epidermolysis bullosa
  publication-title: Br J Dermatol
  contributor:
    fullname: Harper
– volume: 135
  start-page: 603
  year: 1996 Oct
  end-page: 606
  ident: bib37
  article-title: Fatal cardiomyopathy in dystrophic epidermolysis bullosa
  publication-title: Br J Dermatol
  contributor:
    fullname: Sullivan
– start-page: 482
  year: 2007
  end-page: 496
  ident: bib6
  article-title: Clinical paediatric dietetics
  contributor:
    fullname: Haynes
– volume: 24
  start-page: 349
  year: 2008 Mar 20
  end-page: 354
  ident: bib49
  article-title: Non-endoscopic percutaneous gastrostomy placement in children with recessive dystrophic epidermolysis bullosa
  publication-title: Pediatr Surg Int
  contributor:
    fullname: Azizkhan
– volume: 4
  start-page: 277
  year: 2013 May 1
  end-page: 286
  ident: bib19
  article-title: Chronic illness and disordered eating: a discussion of the literature
  publication-title: Adv Nutr
  contributor:
    fullname: Neumark-Sztainer
– volume: 9
  start-page: 1032
  year: 2017 Sep 18
  ident: bib32
  article-title: The metabolic response to stress and infection in critically ill children: the opportunity of an individualized approach
  publication-title: Nutrients
  contributor:
    fullname: Calderini
– volume: 16
  start-page: 138
  year: 2012 Oct
  end-page: 141
  ident: bib17
  article-title: Improvement of renal function in epidermolysis bullosa patients after gluten free diet: two cases
  publication-title: Eur Rev Med Pharmacol Sci
  contributor:
    fullname: Aceto
– volume: 65
  start-page: 1001
  year: 2011 Nov
  end-page: 1009
  ident: bib27
  article-title: Correlates of low bone mass in children with generalized forms of epidermolysis bullosa
  publication-title: J Am Acad Dermatol
  contributor:
    fullname: Arbuckle
– volume: 46
  start-page: 842
  year: 2011 May
  end-page: 847
  ident: bib11
  article-title: Esophageal stenosis in epidermolysis bullosum:a challenge for the endoscopist
  publication-title: J Pediatr Surg
  contributor:
    fullname: di Abriola
– volume: 125
  start-page: 374
  year: 1989 Mar
  end-page: 379
  ident: bib35
  article-title: Blood vitamin and trace metal levels in epidermolysis bullosa
  publication-title: Arch Dermatol
  contributor:
    fullname: Johnson
– volume: 166
  start-page: 354
  year: 2012 Feb
  end-page: 361
  ident: bib24
  article-title: Nutritional outcome in children with severe generalized recessive dystrophic epidermolysis bullosa: a short- and long-term evaluation of gastrostomy and enteral feeding
  publication-title: Br J Dermatol
  contributor:
    fullname: Teillac
– volume: 31
  start-page: 176
  year: 2014 Mar 1
  end-page: 182
  ident: bib18
  article-title: Hand function and quality of life in children with epidermolysis bullosa
  publication-title: Pediatr Dermatol
  contributor:
    fullname: Cornwall
– volume: 164
  start-page: 2300
  year: 2014 Sep 1
  end-page: 2309
  ident: bib54
  article-title: Growth charts for individuals with Rubinstein-Taybi syndrome
  publication-title: Am J Med Genet Part A
  contributor:
    fullname: Hennekam
– volume: vol. 19
  start-page: 255
  year: 2011
  end-page: 263
  ident: bib3
  publication-title: Inherited epidermolysis bullosa - the spectrum of complications
  contributor:
    fullname: Babić
– volume: 199
  start-page: 208
  year: 2012 Jul
  end-page: 212
  ident: bib13
  article-title: Fluoroscopically guided dilation of esophageal strictures in patients with dystrophic epidermolysis bullosa: long-term results
  publication-title: Am J Roentgenol
  contributor:
    fullname: Dourado
– volume: 18
  start-page: 649
  year: 2004 Nov
  end-page: 653
  ident: bib31
  article-title: Vitamin and trace metal levels in recessive dystrophic epidermolysis bullosa
  publication-title: J Eur Acad Dermatol Venereol
  contributor:
    fullname: Dubertret
– volume: 89
  start-page: 395
  year: 1987 Oct
  end-page: 399
  ident: bib34
  article-title: Abnormalities of plasma and erythrocyte essential fatty acid composition in epidermolysis bullosa: influence of treatment with diphenylhydantoin
  publication-title: J Invest Dermatol
  contributor:
    fullname: Carter
– year: 2008
  ident: bib44
  article-title: Nutrition in epidermolysis bullosa for children over 1 year of age
  contributor:
    fullname: Haynes
– volume: 36
  start-page: 579
  year: 2011 Aug
  end-page: 584
  ident: bib9
  article-title: The challenges of meeting nutritional requirements in children and adults with epidermolysis bullosa: proceedings of a multidisciplinary team study day
  publication-title: Clin Exp Dermatol
  contributor:
    fullname: Mellerio
– year: 2018 Apr 17
  ident: bib51
  article-title: Effectiveness of gastrostomy for improving nutritional status and quality of life in patients with epidermolysis bullosa: a systematic review
  publication-title: Br J Dermatol
  contributor:
    fullname: Carvalho
– volume: 28
  start-page: 289
  year: 2010 Apr
  end-page: 301
  ident: bib16
  article-title: Nutrition for children with epidermolysis bullosa
  publication-title: Dermatol Clin
  contributor:
    fullname: Haynes
– year: 2007
  ident: bib2
  article-title: Clinical practice Guidelines for nutrition support in infants and children with epidermolysis bullosa (EB)
  contributor:
    fullname: Haynes
– volume: 16
  start-page: 391
  year: 2014 Oct 20
  end-page: 395
  ident: bib12
  article-title: Oral viscous budesonide as a first-line approach to esophageal stenosis in epidermolysis bullosa: an open-label trial in six children
  publication-title: Pediatr Drugs
  contributor:
    fullname: Gentilino
– volume: 9
  start-page: 76
  year: 2014 May 20
  ident: bib1
  article-title: Multicentre consensus recommendations for skin care in inherited epidermolysis bullosa
  publication-title: Orphanet J Rare Dis
  contributor:
    fullname: Hadj-Rabia
– volume: 28
  start-page: 507
  year: 2016 Aug
  end-page: 516
  ident: bib43
  article-title: Advancement in management of epidermolysis bullosa
  publication-title: Curr Opin Pediatr
  contributor:
    fullname: Teng
– volume: 140
  start-page: 467
  year: 2002 Apr
  end-page: 469
  ident: bib29
  article-title: Bone metabolism in children with epidermolysis bullosa
  publication-title: J Pediatr
  contributor:
    fullname: Palisson
– volume: 94
  start-page: 539
  year: 2015 Jul
  end-page: 546
  ident: bib40
  article-title: Agreement between actual height and estimated height using segmental limb lengths for individuals with cerebral palsy
  publication-title: Am J Phys Med Rehabil
  contributor:
    fullname: Hurvitz
– year: 2016 Dec 23
  ident: bib28
  article-title: Birmingham epidermolysis severity score and vitamin D status are associated with low BMD in children with epidermolysis bullosa
  publication-title: Osteoporos Int
  contributor:
    fullname: Bergamaschi
– volume: 16
  start-page: 173
  year: 2016 Dec 29
  ident: bib36
  article-title: Homocysteine metabolism in children and adolescents with epidermolysis bullosa
  publication-title: BMC Pediatr
  contributor:
    fullname: Consonni
– volume: 46
  start-page: 147
  year: 2008 Feb
  end-page: 158
  ident: bib10
  article-title: Gastrointestinal complications of inherited epidermolysis bullosa: cumulative experience of the national epidermolysis bullosa registry
  publication-title: J Pediatr Gastroenterol Nutr
  contributor:
    fullname: Suchindran
– volume: 88
  start-page: 953
  year: 1993 Jun
  end-page: 955
  ident: bib14
  article-title: Chronic recurrent esophageal strictures treated with balloon dilation in children with autosomal recessive epidermolysis bullosa dystrophica
  publication-title: Am J Gastroenterol
  contributor:
    fullname: Ring
– volume: 8
  start-page: 1462
  year: 2010
  ident: bib39
  article-title: Scientific Opinion on Dietary Reference Values for carbohydrates and dietary fibre
  contributor:
    fullname: European Food Safety Authority (EFSA)
– volume: 127
  start-page: 1
  year: 1971
  end-page: 40
  ident: bib33
  article-title: Reports on public health and medical subjects. No. 127. Report of the expert group on special care for babies
  publication-title: Rep Publ Health Med Subj (Lond)
  contributor:
    fullname: Department of Health and Social Security
– volume: 90
  start-page: 217
  year: 2015 Apr
  end-page: 223
  ident: bib7
  article-title: Nutritional aspects of children and adolescents with epidermolysis bullosa: literature review
  publication-title: An Bras Dermatol
  contributor:
    fullname: Costa
– volume: 143A
  start-page: 2227
  year: 2007 Oct 1
  end-page: 2235
  ident: bib53
  article-title: Weight for age charts for children with achondroplasia
  publication-title: Am J Med Genet Part A
  contributor:
    fullname: Scott
– volume: 5
  start-page: 22
  year: 1988 Feb
  end-page: 27
  ident: bib25
  article-title: Nutritional and metabolic profile of children with epidermolysis bullosa
  publication-title: Pediatr Dermatol
  contributor:
    fullname: McKinney
– volume: 163
  year: 2013 Dec 1
  ident: bib52
  article-title: Patterns of growth in ambulatory males with duchenne muscular dystrophy
  publication-title: J Pediatr
  contributor:
    fullname: Oleszek
– volume: 28
  start-page: 353
  year: 2010 Apr
  end-page: 355
  ident: bib26
  article-title: Osteopenia and osteoporosis in epidermolysis bullosa
  publication-title: Dermatol Clin
  contributor:
    fullname: Mellerio
– volume: 55
  start-page: 264
  year: 2014 Jan
  ident: bib22
  article-title: Nutritional outcomes in children with epidermolysis bullosa: the experiences of two centers in korea
  publication-title: Yonsei Med J
  contributor:
    fullname: Park
– start-page: 2013
  year: 2013
  ident: bib42
  article-title: ISCD official positions - paediatric- international society for clinical densitometry (ISCD)
  contributor:
    fullname: ISCD
– volume: 27
  start-page: 238
  year: 2010 May
  end-page: 243
  ident: bib38
  article-title: Dilated cardiomyopathy in epidermolysis bullosa: a retrospective, multicenter study
  publication-title: Pediatr Dermatol
  contributor:
    fullname: Azizkhan
– volume: 29
  start-page: 277
  year: 2012 May
  end-page: 284
  ident: bib47
  article-title: Gastrostomy tube feeding in children with epidermolysis bullosa: consideration of key issues
  publication-title: Pediatr Dermatol
  contributor:
    fullname: Martinez
– volume: 61
  start-page: 367
  year: 2009 Sep
  end-page: 384
  ident: bib4
  article-title: Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part I. Epithelial associated tissues
  publication-title: J Am Acad Dermatol
  contributor:
    fullname: Mellerio
– volume: 28
  start-page: 357
  year: 2010 Apr
  end-page: 359
  ident: bib23
  article-title: Growth and pubertal delay in patients with epidermolysis bullosa
  publication-title: Dermatol Clin
  contributor:
    fullname: Brain
– volume: 58
  start-page: 621
  year: 2014 May
  end-page: 623
  ident: bib48
  article-title: Use of a novel laparoscopic gastrostomy technique in children with severe epidermolysis bullosa
  publication-title: J Pediatr Gastroenterol Nutr
  contributor:
    fullname: Parikh
– volume: 158
  start-page: 1308
  year: 2008 Jun
  end-page: 1314
  ident: bib8
  article-title: Gastrointestinal complications of epidermolysis bullosa in children
  publication-title: Br J Dermatol
  contributor:
    fullname: Sebire
– volume: 9
  start-page: 594
  issue: 6
  year: 2017
  ident: 10.1016/j.clnu.2019.02.023_bib41
  article-title: Nutritional challenges in duchenne muscular dystrophy
  publication-title: Nutrients
  doi: 10.3390/nu9060594
  contributor:
    fullname: Salera
– volume: 28
  start-page: 357
  issue: 2
  year: 2010
  ident: 10.1016/j.clnu.2019.02.023_bib23
  article-title: Growth and pubertal delay in patients with epidermolysis bullosa
  publication-title: Dermatol Clin
  doi: 10.1016/j.det.2010.01.007
  contributor:
    fullname: Martinez
– volume: 16
  start-page: 138
  issue: 4
  year: 2012
  ident: 10.1016/j.clnu.2019.02.023_bib17
  article-title: Improvement of renal function in epidermolysis bullosa patients after gluten free diet: two cases
  publication-title: Eur Rev Med Pharmacol Sci
  contributor:
    fullname: Annicchiarico
– volume: 29
  start-page: 277
  issue: 3
  year: 2012
  ident: 10.1016/j.clnu.2019.02.023_bib47
  article-title: Gastrostomy tube feeding in children with epidermolysis bullosa: consideration of key issues
  publication-title: Pediatr Dermatol
  doi: 10.1111/j.1525-1470.2011.01612.x
  contributor:
    fullname: Haynes
– volume: 55
  start-page: 181
  issue: 2
  year: 2016
  ident: 10.1016/j.clnu.2019.02.023_bib45
  article-title: Long-term outcomes in adults with recessive dystrophic epidermolysis bullosa fed by a gastrostomy tube in situ
  publication-title: Int J Dermatol
  doi: 10.1111/ijd.12876
  contributor:
    fullname: Hubbard
– start-page: 482
  year: 2007
  ident: 10.1016/j.clnu.2019.02.023_bib6
  contributor:
    fullname: Haynes
– volume: 9
  start-page: 76
  issue: 1
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib1
  article-title: Multicentre consensus recommendations for skin care in inherited epidermolysis bullosa
  publication-title: Orphanet J Rare Dis
  doi: 10.1186/1750-1172-9-76
  contributor:
    fullname: El Hachem
– volume: 61
  start-page: 387
  issue: 3
  year: 2009
  ident: 10.1016/j.clnu.2019.02.023_bib5
  article-title: Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part II. Other organs
  publication-title: J Am Acad Dermatol
  doi: 10.1016/j.jaad.2009.03.053
  contributor:
    fullname: Fine
– volume: 154
  start-page: 959
  issue: 5
  year: 2006
  ident: 10.1016/j.clnu.2019.02.023_bib30
  article-title: Bone mineralization in children with epidermolysis bullosa
  publication-title: Br J Dermatol
  doi: 10.1111/j.1365-2133.2005.07123.x
  contributor:
    fullname: Fewtrell
– volume: 61
  start-page: 367
  issue: 3
  year: 2009
  ident: 10.1016/j.clnu.2019.02.023_bib4
  article-title: Extracutaneous manifestations and complications of inherited epidermolysis bullosa: part I. Epithelial associated tissues
  publication-title: J Am Acad Dermatol
  doi: 10.1016/j.jaad.2009.03.052
  contributor:
    fullname: Fine
– volume: 16
  start-page: 173
  issue: 1
  year: 2016
  ident: 10.1016/j.clnu.2019.02.023_bib36
  article-title: Homocysteine metabolism in children and adolescents with epidermolysis bullosa
  publication-title: BMC Pediatr
  doi: 10.1186/s12887-016-0714-7
  contributor:
    fullname: De Giuseppe
– volume: 9
  start-page: 1032
  issue: 9
  year: 2017
  ident: 10.1016/j.clnu.2019.02.023_bib32
  article-title: The metabolic response to stress and infection in critically ill children: the opportunity of an individualized approach
  publication-title: Nutrients
  doi: 10.3390/nu9091032
  contributor:
    fullname: De Cosmi
– volume: 5
  start-page: 22
  issue: 1
  year: 1988
  ident: 10.1016/j.clnu.2019.02.023_bib25
  article-title: Nutritional and metabolic profile of children with epidermolysis bullosa
  publication-title: Pediatr Dermatol
  doi: 10.1111/j.1525-1470.1988.tb00879.x
  contributor:
    fullname: Lechner-Gruskay
– volume: 135
  start-page: 603
  issue: 4
  year: 1996
  ident: 10.1016/j.clnu.2019.02.023_bib37
  article-title: Fatal cardiomyopathy in dystrophic epidermolysis bullosa
  publication-title: Br J Dermatol
  doi: 10.1111/j.1365-2133.1996.tb03840.x
  contributor:
    fullname: Melville
– volume: vol. 19
  start-page: 255
  year: 2011
  ident: 10.1016/j.clnu.2019.02.023_bib3
  contributor:
    fullname: Murat-Sušić
– start-page: 2013
  year: 2013
  ident: 10.1016/j.clnu.2019.02.023_bib42
  contributor:
    fullname: ISCD
– volume: 27
  start-page: 238
  issue: 3
  year: 2010
  ident: 10.1016/j.clnu.2019.02.023_bib38
  article-title: Dilated cardiomyopathy in epidermolysis bullosa: a retrospective, multicenter study
  publication-title: Pediatr Dermatol
  doi: 10.1111/j.1525-1470.2010.01127.x
  contributor:
    fullname: Lara-Corrales
– year: 2018
  ident: 10.1016/j.clnu.2019.02.023_bib51
  article-title: Effectiveness of gastrostomy for improving nutritional status and quality of life in patients with epidermolysis bullosa: a systematic review
  publication-title: Br J Dermatol
  doi: 10.1111/bjd.16139
  contributor:
    fullname: Zidorio
– volume: 143A
  start-page: 2227
  issue: 19
  year: 2007
  ident: 10.1016/j.clnu.2019.02.023_bib53
  article-title: Weight for age charts for children with achondroplasia
  publication-title: Am J Med Genet Part A
  doi: 10.1002/ajmg.a.31873
  contributor:
    fullname: Hoover-Fong
– volume: 4
  start-page: 277
  issue: 3
  year: 2013
  ident: 10.1016/j.clnu.2019.02.023_bib19
  article-title: Chronic illness and disordered eating: a discussion of the literature
  publication-title: Adv Nutr
  doi: 10.3945/an.112.003608
  contributor:
    fullname: Quick
– start-page: 690
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib15
  contributor:
    fullname: Sklar
– volume: 89
  start-page: 395
  issue: 4
  year: 1987
  ident: 10.1016/j.clnu.2019.02.023_bib34
  article-title: Abnormalities of plasma and erythrocyte essential fatty acid composition in epidermolysis bullosa: influence of treatment with diphenylhydantoin
  publication-title: J Invest Dermatol
  doi: 10.1111/1523-1747.ep12471769
  contributor:
    fullname: Cunnane
– volume: 90
  start-page: 217
  issue: 2
  year: 2015
  ident: 10.1016/j.clnu.2019.02.023_bib7
  article-title: Nutritional aspects of children and adolescents with epidermolysis bullosa: literature review
  publication-title: An Bras Dermatol
  doi: 10.1590/abd1806-4841.20153206
  contributor:
    fullname: Zidorio
– volume: 18
  start-page: 649
  issue: 6
  year: 2004
  ident: 10.1016/j.clnu.2019.02.023_bib31
  article-title: Vitamin and trace metal levels in recessive dystrophic epidermolysis bullosa
  publication-title: J Eur Acad Dermatol Venereol
  doi: 10.1111/j.1468-3083.2004.01067.x
  contributor:
    fullname: Ingen-Housz-Oro
– volume: 28
  start-page: 507
  issue: 4
  year: 2016
  ident: 10.1016/j.clnu.2019.02.023_bib43
  article-title: Advancement in management of epidermolysis bullosa
  publication-title: Curr Opin Pediatr
  doi: 10.1097/MOP.0000000000000380
  contributor:
    fullname: Cohn
– volume: 36
  start-page: 579
  issue: 6
  year: 2011
  ident: 10.1016/j.clnu.2019.02.023_bib9
  article-title: The challenges of meeting nutritional requirements in children and adults with epidermolysis bullosa: proceedings of a multidisciplinary team study day
  publication-title: Clin Exp Dermatol
  doi: 10.1111/j.1365-2230.2011.04091.x
  contributor:
    fullname: Hubbard
– volume: 46
  start-page: 842
  issue: 5
  year: 2011
  ident: 10.1016/j.clnu.2019.02.023_bib11
  article-title: Esophageal stenosis in epidermolysis bullosum:a challenge for the endoscopist
  publication-title: J Pediatr Surg
  doi: 10.1016/j.jpedsurg.2011.02.017
  contributor:
    fullname: De Angelis
– volume: 16
  start-page: 391
  issue: 5
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib12
  article-title: Oral viscous budesonide as a first-line approach to esophageal stenosis in epidermolysis bullosa: an open-label trial in six children
  publication-title: Pediatr Drugs
  doi: 10.1007/s40272-014-0086-0
  contributor:
    fullname: Zanini
– volume: 95
  start-page: 575
  issue: 5
  year: 1995
  ident: 10.1016/j.clnu.2019.02.023_bib21
  article-title: Nutrition management of patients with epidermolysis bullosa
  publication-title: J Am Diet Assoc
  doi: 10.1016/S0002-8223(95)00157-3
  contributor:
    fullname: Birge
– volume: 47
  start-page: 541
  issue: 06
  year: 2015
  ident: 10.1016/j.clnu.2019.02.023_bib50
  article-title: A two-step multidisciplinary approach to treat recurrent esophageal strictures in children with epidermolysis bullosa dystrophica
  publication-title: Endoscopy
  doi: 10.1055/s-0034-1391308
  contributor:
    fullname: Vowinkel
– volume: 134
  start-page: 872
  issue: 5
  year: 1996
  ident: 10.1016/j.clnu.2019.02.023_bib46
  article-title: Gastrostomy and growth in dystrophic epidermolysis bullosa
  publication-title: Br J Dermatol
  doi: 10.1111/j.1365-2133.1996.tb06318.x
  contributor:
    fullname: Haynes
– volume: 8
  start-page: 1462
  issue: 3
  year: 2010
  ident: 10.1016/j.clnu.2019.02.023_bib39
  article-title: Scientific Opinion on Dietary Reference Values for carbohydrates and dietary fibre
  contributor:
    fullname: European Food Safety Authority (EFSA)
– volume: 140
  start-page: 467
  issue: 4
  year: 2002
  ident: 10.1016/j.clnu.2019.02.023_bib29
  article-title: Bone metabolism in children with epidermolysis bullosa
  publication-title: J Pediatr
  doi: 10.1067/mpd.2002.123287
  contributor:
    fullname: Reyes
– volume: 46
  start-page: 147
  issue: 2
  year: 2008
  ident: 10.1016/j.clnu.2019.02.023_bib10
  article-title: Gastrointestinal complications of inherited epidermolysis bullosa: cumulative experience of the national epidermolysis bullosa registry
  publication-title: J Pediatr Gastroenterol Nutr
  doi: 10.1097/MPG.0b013e31812f5667
  contributor:
    fullname: Fine
– volume: 199
  start-page: 208
  issue: 1
  year: 2012
  ident: 10.1016/j.clnu.2019.02.023_bib13
  article-title: Fluoroscopically guided dilation of esophageal strictures in patients with dystrophic epidermolysis bullosa: long-term results
  publication-title: Am J Roentgenol
  doi: 10.2214/AJR.11.8159
  contributor:
    fullname: Spiliopoulos
– year: 2007
  ident: 10.1016/j.clnu.2019.02.023_bib2
  contributor:
    fullname: Haynes
– volume: 65
  start-page: 1001
  issue: 5
  year: 2011
  ident: 10.1016/j.clnu.2019.02.023_bib27
  article-title: Correlates of low bone mass in children with generalized forms of epidermolysis bullosa
  publication-title: J Am Acad Dermatol
  doi: 10.1016/j.jaad.2010.08.028
  contributor:
    fullname: Bruckner
– year: 2016
  ident: 10.1016/j.clnu.2019.02.023_bib28
  article-title: Birmingham epidermolysis severity score and vitamin D status are associated with low BMD in children with epidermolysis bullosa
  publication-title: Osteoporos Int
  contributor:
    fullname: Rodari
– volume: 58
  start-page: 621
  issue: 5
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib48
  article-title: Use of a novel laparoscopic gastrostomy technique in children with severe epidermolysis bullosa
  publication-title: J Pediatr Gastroenterol Nutr
  doi: 10.1097/MPG.0000000000000256
  contributor:
    fullname: Patel
– volume: 31
  start-page: 176
  issue: 2
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib18
  article-title: Hand function and quality of life in children with epidermolysis bullosa
  publication-title: Pediatr Dermatol
  doi: 10.1111/pde.12262
  contributor:
    fullname: Eismann
– volume: 164
  start-page: 2300
  issue: 9
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib54
  article-title: Growth charts for individuals with Rubinstein-Taybi syndrome
  publication-title: Am J Med Genet Part A
  doi: 10.1002/ajmg.a.36654
  contributor:
    fullname: Beets
– volume: 127
  start-page: 1
  year: 1971
  ident: 10.1016/j.clnu.2019.02.023_bib33
  article-title: Reports on public health and medical subjects. No. 127. Report of the expert group on special care for babies
  publication-title: Rep Publ Health Med Subj (Lond)
  contributor:
    fullname: Department of Health and Social Security
– volume: 163
  issue: 6
  year: 2013
  ident: 10.1016/j.clnu.2019.02.023_bib52
  article-title: Patterns of growth in ambulatory males with duchenne muscular dystrophy
  publication-title: J Pediatr
  doi: 10.1016/j.jpeds.2013.08.004
  contributor:
    fullname: West
– volume: 125
  start-page: 374
  issue: 3
  year: 1989
  ident: 10.1016/j.clnu.2019.02.023_bib35
  article-title: Blood vitamin and trace metal levels in epidermolysis bullosa
  publication-title: Arch Dermatol
  doi: 10.1001/archderm.1989.01670150064009
  contributor:
    fullname: Fine
– volume: 28
  start-page: 353
  issue: 2
  year: 2010
  ident: 10.1016/j.clnu.2019.02.023_bib26
  article-title: Osteopenia and osteoporosis in epidermolysis bullosa
  publication-title: Dermatol Clin
  doi: 10.1016/j.det.2010.01.006
  contributor:
    fullname: Martinez
– volume: 88
  start-page: 953
  issue: 6
  year: 1993
  ident: 10.1016/j.clnu.2019.02.023_bib14
  article-title: Chronic recurrent esophageal strictures treated with balloon dilation in children with autosomal recessive epidermolysis bullosa dystrophica
  publication-title: Am J Gastroenterol
  contributor:
    fullname: Heyman
– volume: 55
  start-page: 264
  issue: 1
  year: 2014
  ident: 10.1016/j.clnu.2019.02.023_bib22
  article-title: Nutritional outcomes in children with epidermolysis bullosa: the experiences of two centers in korea
  publication-title: Yonsei Med J
  doi: 10.3349/ymj.2014.55.1.264
  contributor:
    fullname: Kim
– volume: 28
  start-page: 289
  issue: 2
  year: 2010
  ident: 10.1016/j.clnu.2019.02.023_bib16
  article-title: Nutrition for children with epidermolysis bullosa
  publication-title: Dermatol Clin
  doi: 10.1016/j.det.2010.01.010
  contributor:
    fullname: Haynes
– volume: 20
  start-page: 303
  issue: 4
  year: 2003
  ident: 10.1016/j.clnu.2019.02.023_bib20
  article-title: Are children with recessive dystrophic epidermolysis bullosa of low birthweight?
  publication-title: Pediatr Dermatol
  doi: 10.1046/j.1525-1470.2003.20404.x
  contributor:
    fullname: Fox
– volume: 166
  start-page: 354
  issue: 2
  year: 2012
  ident: 10.1016/j.clnu.2019.02.023_bib24
  article-title: Nutritional outcome in children with severe generalized recessive dystrophic epidermolysis bullosa: a short- and long-term evaluation of gastrostomy and enteral feeding
  publication-title: Br J Dermatol
  doi: 10.1111/j.1365-2133.2011.10592.x
  contributor:
    fullname: Colomb
– volume: 94
  start-page: 539
  issue: 7
  year: 2015
  ident: 10.1016/j.clnu.2019.02.023_bib40
  article-title: Agreement between actual height and estimated height using segmental limb lengths for individuals with cerebral palsy
  publication-title: Am J Phys Med Rehabil
  doi: 10.1097/PHM.0000000000000205
  contributor:
    fullname: Haapala
– year: 2008
  ident: 10.1016/j.clnu.2019.02.023_bib44
  contributor:
    fullname: Haynes
– volume: 158
  start-page: 1308
  issue: 6
  year: 2008
  ident: 10.1016/j.clnu.2019.02.023_bib8
  article-title: Gastrointestinal complications of epidermolysis bullosa in children
  publication-title: Br J Dermatol
  doi: 10.1111/j.1365-2133.2008.08507.x
  contributor:
    fullname: Freeman
– volume: 24
  start-page: 349
  issue: 3
  year: 2008
  ident: 10.1016/j.clnu.2019.02.023_bib49
  article-title: Non-endoscopic percutaneous gastrostomy placement in children with recessive dystrophic epidermolysis bullosa
  publication-title: Pediatr Surg Int
  doi: 10.1007/s00383-007-2100-x
  contributor:
    fullname: Stehr
SSID ssj0005378
Score 2.425458
SecondaryResourceType review_article
Snippet Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility....
SourceID proquest
crossref
pubmed
elsevier
SourceType Aggregation Database
Index Database
Publisher
StartPage 343
SubjectTerms Enteral nutrition
Epidermolysis bullosa
Growth retardation
Hypercatabolism
Nutritional status
Undernutrition
Title A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management
URI https://dx.doi.org/10.1016/j.clnu.2019.02.023
https://www.ncbi.nlm.nih.gov/pubmed/30857908
https://search.proquest.com/docview/2190484047
Volume 39
hasFullText 1
inHoldings 1
isFullTextHit
isPrint
link http://utb.summon.serialssolutions.com/2.0.0/link/0/eLvHCXMwnV1NTxsxEB2hVKq4IKAFQgG5EuoFliRrO5vtLUqLUipyKUi5WbZ3VgpKdlF2c-W3d2Y_InqgB6S97Lflsd_M2M_PAJduIJ0b6X6gY0pXVZQMA2dTFZA3d5Q_-ySp9oy8nw2nj-puruc7MGnXwjCtssH-GtMrtG6u9Jra7D0vFr0_nD2wjiWFICxKw4v4WGyL2vTNyyuah6zRmMdZ-Olm4UzN8fLLbMP0rrjS7QzlW87preCzckK3-7DXRI9iXBfwAHYwO4TujwWW4ptoJD6XYtYq7B_Cx_tm7vwT4Fhk7Y2AnVciWkFxUeYCeavY9SqvJEqEo8w0L-x3MbGbAotrYbcKnnSyRuYPVwOLhbBZIlZbEs1neLz9-TCZBs0mC4GXelgGQ6Uj59IRdXaJnsIdL5PQuwQjlTqZWqd8xFSoUDsKPnxK4Ci9tQ4pT6LgMpJH0MnyDE9AYKwIEUYWpVT01YHFVHqq_xg1pqnGLly1tWueay0N05LMngzbwrAtTD-kQ3ZBtwYw_7QIQ2D_3_e-ttYy1FV4_sNmmG8KQ-BMeKX6KurCcW3GbTkkK_3H_dHpO__6BXZDzsQrPvcZdMr1Bs8pXCndRdUeL-DD-Nfv6ewv5jPpzA
link.rule.ids 315,783,787,4511,24130,27938,27939,45599,45693
linkProvider Elsevier
linkToHtml http://utb.summon.serialssolutions.com/2.0.0/link/0/eLvHCXMwnV1LT9wwEB7xkAqXCmiBLS8joV5K2CW2NxtuaAEtLbuXgsTNsp2JtAgStMle-9s7k8eqPcABKZe8LY_9zYz9-TPAiTuXzg10L9AxpasqSvqBs6kKyJs7yp99klR7Ro4n_dGD-vmoH5dg2K6FYVplg_01pldo3VzpNrXZfZ1Ou785e2AdSwpBWJQmXoZVxfpZ1KjP_vzD85A1HPNACz_erJypSV7-OZszvyuuhDtD-ZZ3eiv6rLzQzQZ8bsJHcVmXcBOWMNuCztUUS_FdNBqfz2LSSuxvwadxM3n-BfBSZO2NgL1XIlpFcVHmAnmv2NlLXmmUCEepaV7YCzG08wKLU2EXEp50MkMmEFcji4WwWSJeFiyar_Bwc30_HAXNLguBl7pfBn2lI-fSAfV2iZ7iHS-T0LsEI5U6mVqnfMRcqFA7ij58SugovbUOKVGi6DKS27CS5RnugsBYESQMLEqp6KvnFlPpqf5j1JimGjvwo61d81qLaZiWZfZk2BaGbWF6IR2yA7o1gPmvSRhC-3ffO26tZaiv8ASIzTCfF4bQmQBL9VTUgZ3ajItySJb6j3uDbx_86xGsje7Hd-budvJrD9ZDTssrcvc-rJSzOR5Q7FK6w6pt_gV_4utu
openUrl ctx_ver=Z39.88-2004&ctx_enc=info%3Aofi%2Fenc%3AUTF-8&rfr_id=info%3Asid%2Fsummon.serialssolutions.com&rft_val_fmt=info%3Aofi%2Ffmt%3Akev%3Amtx%3Ajournal&rft.genre=article&rft.atitle=A+nutrition-based+approach+to+epidermolysis+bullosa%3A+Causes%2C+assessments%2C+requirements+and+management&rft.jtitle=Clinical+nutrition+%28Edinburgh%2C+Scotland%29&rft.au=Salera%2C+Simona&rft.au=Tadini%2C+Gianluca&rft.au=Rossetti%2C+Donata&rft.au=Grassi%2C+Francesca+Sofia&rft.date=2020-02-01&rft.eissn=1532-1983&rft.volume=39&rft.issue=2&rft.spage=343&rft.epage=352&rft_id=info:doi/10.1016%2Fj.clnu.2019.02.023&rft.externalDBID=NO_FULL_TEXT
thumbnail_l http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/lc.gif&issn=0261-5614&client=summon
thumbnail_m http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/mc.gif&issn=0261-5614&client=summon
thumbnail_s http://covers-cdn.summon.serialssolutions.com/index.aspx?isbn=/sc.gif&issn=0261-5614&client=summon