A nutrition-based approach to epidermolysis bullosa: Causes, assessments, requirements and management

Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutrition...

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Published inClinical nutrition (Edinburgh, Scotland) Vol. 39; no. 2; pp. 343 - 352
Main Authors Salera, Simona, Tadini, Gianluca, Rossetti, Donata, Grassi, Francesca Sofia, Marchisio, Paola, Agostoni, Carlo, Giavoli, Claudia, Rodari, Giulia, Guez, Sophie
Format Journal Article
LanguageEnglish
Published England Elsevier Ltd 01.02.2020
Subjects
Enteral nutrition
Epidermolysis bullosa
Growth retardation
Hypercatabolism
Nutritional status
Undernutrition
Epidermolysis bullosa
Enteral nutrition
Hypercatabolism
Undernutrition
Growth retardation
Nutritional status
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Summary:Inherited epidermolysis bullosa (EB) is a clinically and genetically heterogeneous group of rare diseases characterized by skin and mucous membrane fragility. EB primarily involves the skin and, in specific subtypes, the mucous membrane, resulting in complications which can strongly affect nutritional status (e.g. gastrointestinal complications, hand deformities, pain). The aims of nutritional support mainly include improving nutritional status, alleviating the stress of oral feeding and minimizing nutritional deficiencies, thus consequently improving growth, pubertal development, bowel function, immune status and wound healing. The aim of this review is to discuss knowledge of different aspects of the disease related to nutrition and growth.
Bibliography:ObjectType-Article-2
SourceType-Scholarly Journals-1
ObjectType-Feature-3
content type line 23
ObjectType-Review-1
ISSN:0261-5614
1532-1983
DOI:10.1016/j.clnu.2019.02.023