A case of incomplete Currarino triad with malignant transformation

• Published in: Pediatric surgery international Vol. 15; no. 5-6; pp. 409 - 410
• Main Authors: TANDER, B, BASKIN, D, BULUT, M
• Format: Journal Article
• Language: English
• Published: Heidelberg Springer 01.07.1999; Berlin Springer Nature B.V
• Subjects: Antineoplastic Combined Chemotherapy Protocols - therapeutic use; Biological and medical sciences; Colostomy; Constriction, Pathologic; Fatal Outcome; Female; Gastroenterology. Liver. Pancreas. Abdomen; Humans; Infant, Newborn; Intestinal Obstruction - congenital; Intestinal Obstruction - diagnostic imaging; Intestinal Obstruction - surgery; Medical sciences; Neoplasm Recurrence, Local - diagnosis; Neoplasm Recurrence, Local - drug therapy; Neoplasm Recurrence, Local - surgery; Rectal Diseases - congenital; Rectal Diseases - surgery; Sacrum; Spinal Neoplasms - congenital; Spinal Neoplasms - diagnosis; Spinal Neoplasms - drug therapy; Spinal Neoplasms - surgery; Stomach. Duodenum. Small intestine. Colon. Rectum. Anus; Syndrome; Teratoma - congenital; Teratoma - diagnosis; Teratoma - drug therapy; Teratoma - surgery; Tomography, X-Ray Computed; Tropical medicine; Tumors; Asia; Turkey; Human; Agenesis; Teratoma; Anorectal; Presacral; Congenital disease; Case study; Concomitant disease; Treatment; Malformation; Malignant transformation; Digestive diseases; Intestinal disease; Tumor; Evolution; Female; Child; Anorectal disease
• ISSN: 0179-0358; 1437-9813
• DOI: 10.1007/s003830050615

A case of an incomplete Currarino triad is reported. The baby underwent an emergency laparotomy due to a life-threatening intestinal obstruction caused by severe rectal stenosis. During the posterosagittal anorectoplasty (PSARP), a presacral teratoma was identified and resected. The tumor recurred three times; she initially responded to chemotherapy, but nonetheless died at the age of 4 years. In cases with evidence of anorectal stenosis, a presacral mass should be suspected. PSARP is the best choice of treatment for both the anorectal anomaly and excision of the presacral mass. The presacral region should be followed up closely for recurrence of the tumor.