Congenital Cranial Dysinnervation Disorder Complicated by Ipsilateral Orbital Choriostoma

A 20-year-old woman with right-sided congenital cranial dysinnervation disorder (exotropia, ophthalmoplegia, and ptosis) presented for strabismus surgery. Exploration of the right eye confirmed abnormal extraocular muscles. Lateral rectus recession with medial rectus plication and inferior oblique r...

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Bibliographic Details
Published inJournal of pediatric ophthalmology and strabismus Vol. 59; no. 6; pp. E66 - e68
Main Author Khan, Arif O
Format Journal Article
LanguageEnglish
Published Thorofare Slack, Inc 01.11.2022
SLACK INCORPORATED
Subjects
Cartilage
Case reports
Congenital diseases
Connective tissue
Cysts
Exocrine glands
Genetic disorders
Inflammation
Strabismus
Surgery
United Arab Emirates
Abu Dhabi United Arab Emirates
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Summary:A 20-year-old woman with right-sided congenital cranial dysinnervation disorder (exotropia, ophthalmoplegia, and ptosis) presented for strabismus surgery. Exploration of the right eye confirmed abnormal extraocular muscles. Lateral rectus recession with medial rectus plication and inferior oblique recession improved primary position ocular alignment. However, an unusual pattern of inferior chemosis developed postoperatively and persisted during the next month. Excision and histologic examination of this tissue revealed areas of lacrimal gland and cartilage with surrounding inflammation, suggestive of a disrupted orbital choriostoma. [J Pediatr Ophthalmol Strabismus. 2022;59(6):e66–e68.]
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
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ISSN:0191-3913
1938-2405
DOI:10.3928/01913913-20220907-01