Xanthogranuloma of the dura in systemic Weber-Christian disease

A 51-year-old woman who had systemic Weber-Christian disease (WCD) displayed multiple xanthomatous lesions and a large xanthogranuloma of the tentorium cerebelli with signs of brainstem and cerebellar compression. Three other cases of dural xanthomatous lesions associated with systemic WCD have been...

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Bibliographic Details
Published inNeurology Vol. 33; no. 8; p. 1067
Main Authors Pick, P, Jean, E, Horoupian, D, Factor, S
Format Journal Article
LanguageEnglish
Published United States 01.08.1983
Subjects
Dura Mater - pathology
Female
Granuloma - complications
Granuloma - pathology
Humans
Middle Aged
Panniculitis, Nodular Nonsuppurative - complications
Panniculitis, Nodular Nonsuppurative - pathology
Xanthomatosis - complications
Xanthomatosis - pathology
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Summary:A 51-year-old woman who had systemic Weber-Christian disease (WCD) displayed multiple xanthomatous lesions and a large xanthogranuloma of the tentorium cerebelli with signs of brainstem and cerebellar compression. Three other cases of dural xanthomatous lesions associated with systemic WCD have been reported. These dural and leptomeningeal xanthomatous lesions in WCD, a nonsuppurative inflammatory condition, are similar to those of Hand-Schüller-Christian disease, a quasi-neoplastic process.
ISSN:0028-3878
DOI:10.1212/WNL.33.8.1067