Auditory neuropathy/dyssynchrony: its diagnosis and management

Patients with auditory neuropathy/dyssynchrony exhibit no auditory brain stem response (ABR), no middle ear muscle response, and both normal otoacoustic emissions or normal cochlear microphonics. An absent or grossly abnormal ABR is not always associated with deafness. In contrast, a hearing loss of...

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Bibliographic Details
Published inThe Pediatric clinics of North America Vol. 50; no. 2; p. 331
Main Authors Berlin, Charles I, Morlet, Thierry, Hood, Linda J
Format Journal Article
LanguageEnglish
Published United States 01.04.2003
Subjects
Audiometry, Pure-Tone
Auditory Diseases, Central - diagnosis
Auditory Diseases, Central - physiopathology
Auditory Diseases, Central - therapy
Child
Cochlea - physiopathology
Cochlear Implantation
Cochlear Nerve - physiopathology
Evoked Potentials, Auditory, Brain Stem - physiology
Hearing Aids
Humans
Otoacoustic Emissions, Spontaneous - physiology
Peripheral Nerves - physiopathology
Time Factors
Verbal Learning
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Summary:Patients with auditory neuropathy/dyssynchrony exhibit no auditory brain stem response (ABR), no middle ear muscle response, and both normal otoacoustic emissions or normal cochlear microphonics. An absent or grossly abnormal ABR is not always associated with deafness. In contrast, a hearing loss of 30 dB or more usually predicts absent otoacoustic emissions, but normal emissions can be seen in some patients whose behavioral audiograms imply total deafness. This article reviews the underlying physiology that makes these tests both useful and potentially misleading, and recommends steps to be considered by primary care physicians and other professionals to compensate for the vulnerabilities of each of the procedures.
ISSN:0031-3955
DOI:10.1016/S0031-3955(03)00031-2