Atypical Kawasaki disease: an often missed diagnosis

We describe four patients with vasculitis of the coronary and other medium sized arteries. Three of them died as a consequence of cardiac failure and the fourth had a ruptured aneurysm of the left common iliac artery. Coronary vasculitis is pathognomonic for Kawasaki disease (KD), but our patients h...

Full description

Saved in:
Bibliographic Details
Published inEuropean journal of pediatrics Vol. 151; no. 8; p. 577
Main Authors Boven, K, De Graeff-Meeder, E R, Spliet, W, Kuis, W
Format Journal Article
LanguageEnglish
Published Germany 01.08.1992
Subjects
Child, Preschool
Coronary Vessels - pathology
Humans
Infant
Male
Mucocutaneous Lymph Node Syndrome - diagnosis
Mucocutaneous Lymph Node Syndrome - pathology
Myocardium - pathology
Online AccessGet more information

Cover

More Information
Summary:We describe four patients with vasculitis of the coronary and other medium sized arteries. Three of them died as a consequence of cardiac failure and the fourth had a ruptured aneurysm of the left common iliac artery. Coronary vasculitis is pathognomonic for Kawasaki disease (KD), but our patients had few other signs of this disorder, suggesting so called atypical KD. Because the described patients lacked most of the clinical criteria, the diagnosis was delayed. We focus on other clinical features in these patients and stress the importance of early recognition and treatment.
ISSN:0340-6199
DOI:10.1007/BF01957725