Keratosis follicularis spinulosa decalvans and acne keloidalis nuchae

• Published in: Australasian journal of dermatology Vol. 46; no. 4; pp. 257 - 260
• Main Authors: Goh, Michelle SY, Magee, Jill, Chong, Alvin H
• Format: Journal Article
• Language: English
• Published: Melbourne, Australia Blackwell Science Pty 01.11.2005; Blackwell
• Subjects: Acne Keloid - diagnosis; Acne Keloid - drug therapy; Acne Keloid - etiology; Adult; Alopecia - etiology; Anti-Bacterial Agents - therapeutic use; Anti-Inflammatory Agents - therapeutic use; Biological and medical sciences; Darier Disease - complications; Darier Disease - diagnosis; Darier Disease - drug therapy; Dermatology; Dyskeratosis; Eyebrows; Humans; isotretinoin; Isotretinoin - therapeutic use; keratosis pilaris; keratosis pilaris atrophicans; Male; Medical sciences; Neck; retinoid; Scalp Dermatoses - diagnosis; Scalp Dermatoses - drug therapy; Scalp Dermatoses - etiology; scarring alopecia; Treatment Outcome; Acne keloidalis; Human; Dyskeratosis; Skin disease; Dermatology; Hyperkeratosis; Retinoid; Folliculitis; Genetic disease; Case study; keratosis pilaris; Chemotherapy; Treatment; Keratosis follicularis spinulosa decalvans; Scalp; Isotretinoin; Neck; keratosis pilaris atrophicans; Scarring alopecia; Pilaris keratosis
• ISSN: 0004-8380; 1440-0960
• DOI: 10.1111/j.1440-0960.2005.00196.x

SUMMARY A 27‐year‐old man presented with a 10‐year history of scarring alopecia on the vertex of the scalp associated with follicular crusting and pustule formation, and a papular eruption on the posterior neck. Additionally, there was keratosis pilaris on the cheeks, eyebrows and thighs. Histology from the vertex showed scarring with a mixed perifollicular inflammatory infiltrate and foci of acute suppurative folliculitis. With clinical correlation, the diagnosis of keratosis follicularis spinulosa decalvans and concurrent acne keloidalis nuchae was made. The association of keratosis follicularis spinulosa decalvans with acne keloidalis nuchae has not previously been described. The patient responded to treatment with oral isotretinoin 20 mg (0.25 mg/kg) daily for 12 months.