Intramyocardial angiomyolipoma

We report a case of cardiac angiomyolipoma in a 48-year-old woman who went to the hospital because of shortness of breath. Cardiac ultrasonography showed a right atrial mass, which was surgically removed. Pathologic examination revealed a 6-cm-diameter, dome-shaped mass composed of a mixture of bloo...

Full description

Saved in:
Bibliographic Details
Published inThe American journal of surgical pathology Vol. 18; no. 11; p. 1164
Main Authors Shimizu, M, Manabe, T, Tazelaar, H D, Hirokawa, M, Moriya, T, Ito, J, Hamanaka, S, Hata, T
Format Journal Article
LanguageEnglish
Published United States 01.11.1994
Subjects
Angiomyolipoma - diagnostic imaging
Angiomyolipoma - pathology
Female
Heart Neoplasms - diagnostic imaging
Heart Neoplasms - pathology
Humans
Middle Aged
Myocardium - pathology
Ultrasonography
Online AccessGet more information

Cover

More Information
Summary:We report a case of cardiac angiomyolipoma in a 48-year-old woman who went to the hospital because of shortness of breath. Cardiac ultrasonography showed a right atrial mass, which was surgically removed. Pathologic examination revealed a 6-cm-diameter, dome-shaped mass composed of a mixture of blood vessels, smooth muscle, and fat. Because of its distinctive morphology and location, we diagnosed it as an intramyocardial angiomyolipoma. There was no evidence of tuberous sclerosis. Since excision of the mass, the patient has remained well without recurrence for 20 months. Angiomyolipomas usually develop in the kidney; extrarenal occurrence is rare. To date, no case of a cardiac angiomyolipoma has been reported in the English literature. The histogenesis of angiomyolipoma is uncertain, but it is most likely hamartomatous in nature.
ISSN:0147-5185
DOI:10.1097/00000478-199411000-00011