Giant Mesenchymal Hamartoma of the Liver in an Adult

• Published in: Nippon Shokaki Geka Gakkai zasshi Vol. 44; no. 5; pp. 526 - 532
• Main Authors: Okaya, Tomohisa, Sugano, Isamu, Hayashi, Shinichi, Suzuki, Hirofumi, Sugimoto, Katsumi, Karaki, Hirokazu, Sasaki, Takehide, Yamamoto, Kazuo, Kato, Masahisa, Yamamori, Hideo
• Format: Journal Article
• Language: English; Japanese
• Published: The Japanese Society of Gastroenterological Surgery 2011
• Subjects: adult; liver; mesenchymal hamartoma
• ISSN: 0386-9768; 1348-9372
• DOI: 10.5833/jjgs.44.526

A 47-year-old woman was admitted to our hospital due to an upper abdominal mass and abdominal distension. Abdominal CT showed a giant multilocular cystic lesion with a maximum dimension of 25cm in the right lobe of the liver and multiple cysts in the left lobbe of the liver. Coarse calcification along the septa was found. Three-dimensional CT cholangiogram showed no findings of communication between the giant multilocular cystic lesion and the biliary tract. MRI showed a variety of low intensity levels on T1-weighted images and a variety of high intensity levels on T2-weighted images in the giant multilocular cystic lesion. Extended right hepatectomy was performed for the giant multilocular cystic lesion in the right liver, and unroofing was performed for the cysts in the left liver. Microscopic findings showed many cysts varying in size with fibrous stroma, proliferated small bile ducts of various sizesand peliosis-like hepatic remnant and lymphangiomatous lesions. The pathological diagnosis was mesenchymal hamartoma of the liver. Mesenchymal hamartoma of the liver is very rare in adults, but should be taken into account for a multilocular cystic lesion in the liver.