Tricuspid Atresia with Absent Pulmonary Valve with Nearly Discontinuous Branch Pulmonary Arteries

Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically signific...

Full description

Saved in:
Bibliographic Details
Published inPediatric cardiology Vol. 45; no. 2; pp. 446 - 451
Main Authors Jin, Justin B., Robinson, Joshua D., Camarda, Joseph A., Satzer, Michael B., Carr, Michael R., Monge, Michael, Patel, Angira
Format Journal Article
LanguageEnglish
Published New York Springer US 01.02.2024
Subjects
Cardiac Surgery
Cardiology
Case Report
Heart Defects, Congenital - surgery
Humans
Infant, Newborn
Male
Medicine
Medicine & Public Health
Pulmonary Artery - diagnostic imaging
Pulmonary Atresia - diagnostic imaging
Pulmonary Atresia - surgery
Pulmonary Valve - abnormalities
Pulmonary Valve - diagnostic imaging
Tricuspid Atresia - diagnostic imaging
Tricuspid Atresia - surgery
Vascular Surgery
Ventricular Septum
Absent pulmonary valve
Interventricular septum
Single ventricle
Hypoplastic right ventricle
Tricuspid atresia
Online AccessGet full text

Cover

More Information
Summary:Absent pulmonary valve with tricuspid atresia or tricuspid stenosis (APV-TA/TS) is an extremely rare congenital heart defect associated with significant morbidity and mortality. Compared to Tetralogy of Fallot with Absent Pulmonary Valve Syndrome, branch pulmonary arteries are not typically significantly dilated. We present the case of a newborn male prenatally diagnosed APV-TA with intact ventricular septum (IVS) and nearly discontinuous branch pulmonary arteries, the surgical strategy employed, and the salient hemodynamic factors considered in the medical decision-making.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
content type line 23
ObjectType-Report-1
ObjectType-Article-3
ISSN:0172-0643
1432-1971
DOI:10.1007/s00246-023-03331-6