A case of unicuspid aortic valve associated with a single coronary artery and ventricular septal defect

• Published in: Journal of medical ultrasonics (2001) Vol. 32; no. 2; pp. 65 - 70
• Main Authors: Ishigami, Hiroko, Iwase, Masatsugu, Hyoudo, Keiko, Aoyama, Idumi, Ito, Mamoru, Tajima, Kazuki, Hasegawa, Kazuo, Tsuboi, Naoya
• Format: Journal Article
• Language: English
• Published: Japan Springer Nature B.V 01.06.2005
• Subjects: Abnormalities; Angiography; Aorta; Coronary vessels; Defects; Heart valves; Literature reviews; Tachycardia; Doppler ultrasonography; aortic valve regurgitation; unicuspid aortic valve
• ISSN: 1346-4523; 1613-2254
• DOI: 10.1007/s10396-005-0037-z

The patient was a 26-year-old man who had undergone patch closure of a ventricular septal defect at 2 years of age. After this surgery, his condition was satisfactory until he visited our hospital for treatment of paroxysmal supraventricular tachycardia in November 2000. Echocardiography revealed moderate to severe aortic valve regurgitation and dilatation of the left ventricle and ascending aorta. These echocardiographic abnormalities were attributed to a bicuspid aortic valve. Coronary angiography suggested the presence of a single coronary artery originating from the left Valsalva sinus. We performed Bentall's operation in January 2003. The intraoperative findings revealed that the aortic valve consisted of an extensively calcified single cusp, and there was a single coronary artery originating from the left Valsalva sinus. Because adult patients with a unicuspid aortic valve are rare, and no cases of unicuspid aortic valve associated with a single coronary artery have been reported, we herein report this case with a review of the literature.