Applying the ACR/EULAR Systemic Sclerosis Classification Criteria to the Spanish Scleroderma Registry Cohort

• Published in: Journal of rheumatology Vol. 42; no. 12; p. 2327
• Main Authors: Sáez-Comet, Luis, Simeón-Aznar, Carmen Pilar, Pérez-Conesa, Mercedes, Vallejo-Rodríguez, Carmen, Tolosa-Vilella, Carles, Iniesta-Arandia, Nerea, Colunga-Argüelles, Dolores, Egurbide-Arberas, Maria Victoria, Ortego-Centeno, Norberto, Vargas-Hitos, José Antonio, Freire-Dapena, Mayka, Rubio-Rivas, Manuel, Ríos-Blanco, Juan José, Trapiella-Martínez, Luis, Fonollosa-Pla, Vicent
• Format: Journal Article
• Language: English
• Published: Canada 01.12.2015
• Subjects: Adult; Cohort Studies; Cross-Sectional Studies; Europe; Female; Humans; Male; Middle Aged; Registries; Scleroderma, Systemic - classification; Scleroderma, Systemic - epidemiology; Scleroderma, Systemic - physiopathology; Severity of Illness Index; Spain; United States; United States; Europe; Spain; SYSTEMIC SCLEROSIS; CLASSIFICATION CRITERIA
• ISSN: 0315-162X
• DOI: 10.3899/jrheum.150144

To compare American College of Rheumatology/European League Against Rheumatism (ACR/EULAR) classification criteria for systemic sclerosis (SSc) with previous American Rheumatology Association (ARA) criteria. This was a cross-sectional multicenter study comparing sensitivity of both criteria in the cutaneous subsets in the Spanish scleroderma registry (RESCLE) cohort. In 1222 patients with SSc, the most prevalent items were Raynaud phenomenon (95%), skin thickening (91%), and abnormal capillaroscopy (89%). ARA criteria classified as SSc 63.5% of all patients, and 63%, 100%, 11.2%, and 0% in the limited, diffuse, sine, and pre-SSc subsets, respectively. ACR/EULAR criteria classified 87.5% of all patients and 98.5%, 100%, 41.8%, and 15.9% in the same subsets, respectively. ACR/EULAR criteria are more sensitive than ARA criteria, especially in limited, sine, and pre-SSc subsets.