Paraganglioma in association with renal artery aneurysm in a 12-year-old male

• Published in: The American surgeon Vol. 77; no. 3; pp. E41 - 42
• Main Authors: Romero González, Rey Jesús, Gutierrez, Eduardo Vásquez, Borroel, Rafael Valdés, Siller Aguirre, Alberto Jerónimo, Delgado, Oziel Cantú, Barnett, Shari, González, Fabián Contreras
• Format: Journal Article
• Language: English
• Published: United States SAGE PUBLICATIONS, INC 01.03.2011
• Subjects: Adolescent; Aneurysm - complications; Aneurysm - surgery; Aneurysms; Humans; Hypertension; Lymph Node Excision; Male; Nephrectomy; Paraganglioma, Extra-Adrenal - complications; Paraganglioma, Extra-Adrenal - surgery; Pheochromocytoma - complications; Pheochromocytoma - surgery; Recurrence; Renal Artery - surgery; Reoperation; Vascular Neoplasms - complications; Vascular Neoplasms - surgery; Vascular Surgical Procedures; Veins & arteries
• ISSN: 0003-1348; 1555-9823
• DOI: 10.1177/000313481107700302

In 2004, the World Health Or- ganization Classification of Endocrine tumors defined PCC as a intraadrenal paraganglioma, whereas closely related tumors of extraadrenal sympathetic or parasym- pathetic paraganglia are classified as an extraadrenal paraganglioma.1 Otherwise, renal artery aneurysms, which are most frequently asymptomatic, are rare, with a reported incidence of between 0.01 per cent in autopsy studies and 0.7 to 1.0 per cent in large-scale screening studies with various imaging modalities.2 We present the case of a 12-year-old male with extra- adrenal pheochromocytoma or paraganglioma associ- ated to a right renal artery aneurysm. The association between PCC and other kinds of an- eurysms is reported in the literature in some papers.4 In a revision, on the pudmed database (keywords: aneu- rysm, aneurysms, pheochromocytoma, paraganglioma), we found 20 cases of aneurysm in association with PCC, including this case (Table 1).