Aberrant left coronary artery arising from the right sinus of Valsalva with a right coronary arteriovenous malformation

• Published in: Pediatric cardiology Vol. 18; no. 5; pp. 385 - 388
• Main Authors: Phoon, C K, Van Son, J, Moore, P A, Brook, M M, Haas, G S, Higgins, C B
• Format: Journal Article
• Language: English
• Published: United States 01.09.1997
• Subjects: Arteriovenous Malformations - diagnosis; Arteriovenous Malformations - physiopathology; Arteriovenous Malformations - surgery; Cardiac Catheterization; Child; Coronary Vessel Anomalies - diagnosis; Coronary Vessel Anomalies - physiopathology; Coronary Vessel Anomalies - surgery; Humans; Male; Myocardial Ischemia - etiology; Sinus of Valsalva - abnormalities
• ISSN: 0172-0643; 1432-1971
• DOI: 10.1007/s002469900208

An 11-year-old boy presented with myocardial ischemia and was found to have an aberrant left main coronary artery from the right sinus of Valsalva coursing between the aorta and pulmonary artery, as well as a small arteriovenous malformation from a right atrial branch of the right coronary artery to the right atrium. Distinctive echocardiographic findings were supported by angiographic and magnetic resonance imaging studies. Treadmill and scintigraphic stress testing were normal. Corrective surgery was accomplished by a modified technique to unroof the intramural proximal course of the left coronary artery, without postoperative complications. The anatomy and pathophysiology of this rare coronary lesion are reviewed.