Orbital desmoplastic small round cell tumor in an infant

Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive malignancy that primarily involves the serosal surfaces of the abdomen and pelvis and has a poor prognosis. Orbital involvement is extremely rare. We report the case of a 2-month-old boy who presented with a right infraorbital mass co...

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Bibliographic Details
Published inDigital journal of ophthalmology Vol. 24; no. 4; pp. 31 - 35
Main Authors Huang, Amy, Patel, Nishita
Format Journal Article
LanguageEnglish
Published United States Massachusetts Eye and Ear Infirmary 31.12.2018
Subjects
Case Report
Desmoplastic Small Round Cell Tumor - diagnosis
Diagnosis, Differential
Humans
Infant
Male
Orbital Neoplasms - diagnosis
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Summary:Desmoplastic small round cell tumor (DSRCT) is a rare, aggressive malignancy that primarily involves the serosal surfaces of the abdomen and pelvis and has a poor prognosis. Orbital involvement is extremely rare. We report the case of a 2-month-old boy who presented with a right infraorbital mass consistent with a DSRCT and causing mass effect and superonasal globe displacement. To our knowledge, this is the first case of orbital DSRCT in an infant.
ISSN:1542-8958
1542-8958
DOI:10.5693/djo.02.2018.10.001