Orthognathic surgery for a patient with trichorhinophalangeal syndrome type I: A case report

Trichorhinophalangeal syndrome (TRPS) type I is characterized by slowly progressing systemic osseous dysplasia, exhibiting craniofacial and other skeletal deformities. However, there have been few reports describing this syndrome after undergoing orthognathic surgery. In this report, we present a pa...

Full description

Saved in:
Bibliographic Details
Published inOral surgery, oral medicine, oral pathology, oral radiology and endodontics Vol. 101; no. 2; pp. e23 - e27
Main Authors Kunimori, Kentaro, Harada, Kiyoshi, Maruoka, Yutaka, Omura, Ken
Format Journal Article
LanguageEnglish
Published United States Mosby, Inc 01.02.2006
Subjects
Abnormalities, Multiple
Adult
Alopecia - genetics
Cephalometry
Dentistry
DNA-Binding Proteins - genetics
Female
Finger Phalanges - abnormalities
Hand Deformities, Congenital - genetics
Humans
Jaw Abnormalities - genetics
Jaw Abnormalities - surgery
Malocclusion, Angle Class III - surgery
Neoplasm Proteins - genetics
Nose - abnormalities
Oral Surgical Procedures
Osteochondrodysplasias - genetics
Osteochondrodysplasias - surgery
Osteotomy, Le Fort
Syndrome
Transcription Factors
Online AccessGet full text

Cover

More Information
Summary:Trichorhinophalangeal syndrome (TRPS) type I is characterized by slowly progressing systemic osseous dysplasia, exhibiting craniofacial and other skeletal deformities. However, there have been few reports describing this syndrome after undergoing orthognathic surgery. In this report, we present a patient with TRPS I who successfully underwent orthognathic surgery. In addition, we examined the skeletal stability of the patient for 2 years after the surgery.
Bibliography:ObjectType-Case Study-2
SourceType-Scholarly Journals-1
ObjectType-Feature-4
content type line 23
ObjectType-Report-1
ObjectType-Article-3
ISSN:1079-2104
1528-395X
DOI:10.1016/j.tripleo.2005.07.014